Atrioventricular septal defect in an adult patient: There are ‘clefts’ and clefts

In this report, we present the case of an adult male with severe mitral regurgitation due to an atrioventricular septal defect. Anatomical assessment by two- and three-dimensional transesophageal echocardiography was essential for detailed morphological characterization and surgical planning. The di...

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Bibliographic Details
Main Authors: Nuno Moreno, Jorge Almeida, Mário Jorge Amorim
Format: Article
Language:English
Published: Elsevier 2016-03-01
Series:Revista Portuguesa de Cardiologia (English Edition)
Online Access:http://www.sciencedirect.com/science/article/pii/S2174204916000428
Description
Summary:In this report, we present the case of an adult male with severe mitral regurgitation due to an atrioventricular septal defect. Anatomical assessment by two- and three-dimensional transesophageal echocardiography was essential for detailed morphological characterization and surgical planning. The different features of a ‘cleft’ in an atrioventricular septal defect compared to an anterior leaflet cleft in an otherwise normal mitral valve are here discussed. Resumo: Os autores apresentam o caso de um doente adulto com regurgitação mitral severa no contexto de um defeito do septo auriculoventricular. A avaliação conjunta por ETE 2 D e 3 D foi fundamental para a caracterização anátomo-funcional da válvula e orientação do procedimento cirúrgico. As particularidades anatómicas de uma «fenda» em contexto de defeito do septo auriculoventricular e de uma fenda numa válvula mitral são aqui discutidas. Keywords: Mitral cleft, Three-dimensional transoesophageal echocardiography, Atrioventricular septal defect, Palavras-chave: Fenda mitral, Ecocardiografia tridimensional, Defeito do septo auriculoventricular
ISSN:2174-2049