Electrical storm in an acquired short QT syndrome successfully treated with quinidine

Abstract Short QT syndrome (SQTS) is a malignant heart disorder defined by the presence of ventricular arrhythmias causing syncope and sudden cardiac arrest. The prevalence in the pediatric population is 0.05%. Quinidine is an established agent for pharmacological prophylaxis in SQTS patients, but c...

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Bibliographic Details
Main Authors: Michael Spartalis, Efthimios Livanis, Eleftherios Spartalis, Alexandros Tsoutsinos
Format: Article
Language:English
Published: Wiley 2019-08-01
Series:Clinical Case Reports
Subjects:
Online Access:https://doi.org/10.1002/ccr3.2282

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