Incomplete Form of Shone Complex in an Adult Congenital Heart Disease Patient

• Main Authors: Beatrice Chia-Hui Shih, Jae Hong Lim, Jooncheol Min, Eung Re Kim, Jae Gun Kwak, Woong-Han Kim
• Format: Article
• Language: English
• Published: Korean Society for Thoracic and Cardiovascular Surgery 2019-04-01
• Series: Korean Journal of Thoracic and Cardiovascular Surgery
• Subjects: Shone’s complex; Bicuspid aortic valve; Parachute mitral valve; Extraanatomic bypass; Aortic coarctation

Shone complex is a rare congenital disorder that involves 4 obstructive lesions of the left heart, as follows: parachute mitral valve, supravalvular mitral ring, subaortic stenosis, and coarctation of the aorta. Incomplete forms with 2 or 3 of these lesions in adult patients have been rarely reported in the literature, meaning that insufficient general data exist concerning the surgical strategy and clinical follow-up. Herein, we report the case of a 31-year-old woman with a diagnosis of incomplete form of Shone complex with parachute mitral valve and coarctation of the aorta who underwent successful single-stage surgical repair.