Childhood Hypopigmented Mycosis Fungoides: A Rare Diagnosis
Primary cutaneous lymphomas (PCL) are rare in pediatrics. Mycosis fungoides (MF) is the most frequent PCL diagnosed in childhood. There are various clinical variants of MF, including the hypopigmented MF (HMF). We present a 5-year-old boy with an 18-month history of progressive, generalized, nonprur...
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doaj-abd1600582d54f378b1578c2d15e86122020-11-25T00:30:57ZengHindawi LimitedCase Reports in Pediatrics2090-68032090-68112016-01-01201610.1155/2016/85643898564389Childhood Hypopigmented Mycosis Fungoides: A Rare DiagnosisCláudia Patraquim0Maria Miguel Gomes1Carla Garcez2Filipa Leite3Tereza Oliva4António Santos5Armando Pinto6Pediatrics Department, Hospital de Braga, Sete Fontes, São Victor, 4710-243 Braga, PortugalPediatrics Department, Hospital de Braga, Sete Fontes, São Victor, 4710-243 Braga, PortugalPediatrics Department, Hospital de Braga, Sete Fontes, São Victor, 4710-243 Braga, PortugalPediatrics Department, Portuguese Oncology Institute of Porto Francisco Gentil, 4200-072 Porto, PortugalPediatrics Department, Portuguese Oncology Institute of Porto Francisco Gentil, 4200-072 Porto, PortugalDermatology Department, Portuguese Oncology Institute of Porto Francisco Gentil, 4200-072 Porto, PortugalPediatrics Department, Portuguese Oncology Institute of Porto Francisco Gentil, 4200-072 Porto, PortugalPrimary cutaneous lymphomas (PCL) are rare in pediatrics. Mycosis fungoides (MF) is the most frequent PCL diagnosed in childhood. There are various clinical variants of MF, including the hypopigmented MF (HMF). We present a 5-year-old boy with an 18-month history of progressive, generalized, nonpruritic hypopigmented lesions with central lacy erythema. He had no improvement with emollients. Skin biopsy showed typical features of HMF. He was treated with topical corticosteroids and tacrolimus and narrow-band ultraviolet B (NBUVB) phototherapy, with good response. HMF may mimic multiple skin disorders. Unusual hypopigmented skin lesions should be biopsied. Though phototherapy is effective, recurrence is common.http://dx.doi.org/10.1155/2016/8564389 |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Cláudia Patraquim Maria Miguel Gomes Carla Garcez Filipa Leite Tereza Oliva António Santos Armando Pinto |
spellingShingle |
Cláudia Patraquim Maria Miguel Gomes Carla Garcez Filipa Leite Tereza Oliva António Santos Armando Pinto Childhood Hypopigmented Mycosis Fungoides: A Rare Diagnosis Case Reports in Pediatrics |
author_facet |
Cláudia Patraquim Maria Miguel Gomes Carla Garcez Filipa Leite Tereza Oliva António Santos Armando Pinto |
author_sort |
Cláudia Patraquim |
title |
Childhood Hypopigmented Mycosis Fungoides: A Rare Diagnosis |
title_short |
Childhood Hypopigmented Mycosis Fungoides: A Rare Diagnosis |
title_full |
Childhood Hypopigmented Mycosis Fungoides: A Rare Diagnosis |
title_fullStr |
Childhood Hypopigmented Mycosis Fungoides: A Rare Diagnosis |
title_full_unstemmed |
Childhood Hypopigmented Mycosis Fungoides: A Rare Diagnosis |
title_sort |
childhood hypopigmented mycosis fungoides: a rare diagnosis |
publisher |
Hindawi Limited |
series |
Case Reports in Pediatrics |
issn |
2090-6803 2090-6811 |
publishDate |
2016-01-01 |
description |
Primary cutaneous lymphomas (PCL) are rare in pediatrics. Mycosis fungoides (MF) is the most frequent PCL diagnosed in childhood. There are various clinical variants of MF, including the hypopigmented MF (HMF). We present a 5-year-old boy with an 18-month history of progressive, generalized, nonpruritic hypopigmented lesions with central lacy erythema. He had no improvement with emollients. Skin biopsy showed typical features of HMF. He was treated with topical corticosteroids and tacrolimus and narrow-band ultraviolet B (NBUVB) phototherapy, with good response. HMF may mimic multiple skin disorders. Unusual hypopigmented skin lesions should be biopsied. Though phototherapy is effective, recurrence is common. |
url |
http://dx.doi.org/10.1155/2016/8564389 |
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