Childhood Hypopigmented Mycosis Fungoides: A Rare Diagnosis

Primary cutaneous lymphomas (PCL) are rare in pediatrics. Mycosis fungoides (MF) is the most frequent PCL diagnosed in childhood. There are various clinical variants of MF, including the hypopigmented MF (HMF). We present a 5-year-old boy with an 18-month history of progressive, generalized, nonprur...

Full description

Bibliographic Details
Main Authors: Cláudia Patraquim, Maria Miguel Gomes, Carla Garcez, Filipa Leite, Tereza Oliva, António Santos, Armando Pinto
Format: Article
Language:English
Published: Hindawi Limited 2016-01-01
Series:Case Reports in Pediatrics
Online Access:http://dx.doi.org/10.1155/2016/8564389
id doaj-abd1600582d54f378b1578c2d15e8612
record_format Article
spelling doaj-abd1600582d54f378b1578c2d15e86122020-11-25T00:30:57ZengHindawi LimitedCase Reports in Pediatrics2090-68032090-68112016-01-01201610.1155/2016/85643898564389Childhood Hypopigmented Mycosis Fungoides: A Rare DiagnosisCláudia Patraquim0Maria Miguel Gomes1Carla Garcez2Filipa Leite3Tereza Oliva4António Santos5Armando Pinto6Pediatrics Department, Hospital de Braga, Sete Fontes, São Victor, 4710-243 Braga, PortugalPediatrics Department, Hospital de Braga, Sete Fontes, São Victor, 4710-243 Braga, PortugalPediatrics Department, Hospital de Braga, Sete Fontes, São Victor, 4710-243 Braga, PortugalPediatrics Department, Portuguese Oncology Institute of Porto Francisco Gentil, 4200-072 Porto, PortugalPediatrics Department, Portuguese Oncology Institute of Porto Francisco Gentil, 4200-072 Porto, PortugalDermatology Department, Portuguese Oncology Institute of Porto Francisco Gentil, 4200-072 Porto, PortugalPediatrics Department, Portuguese Oncology Institute of Porto Francisco Gentil, 4200-072 Porto, PortugalPrimary cutaneous lymphomas (PCL) are rare in pediatrics. Mycosis fungoides (MF) is the most frequent PCL diagnosed in childhood. There are various clinical variants of MF, including the hypopigmented MF (HMF). We present a 5-year-old boy with an 18-month history of progressive, generalized, nonpruritic hypopigmented lesions with central lacy erythema. He had no improvement with emollients. Skin biopsy showed typical features of HMF. He was treated with topical corticosteroids and tacrolimus and narrow-band ultraviolet B (NBUVB) phototherapy, with good response. HMF may mimic multiple skin disorders. Unusual hypopigmented skin lesions should be biopsied. Though phototherapy is effective, recurrence is common.http://dx.doi.org/10.1155/2016/8564389
collection DOAJ
language English
format Article
sources DOAJ
author Cláudia Patraquim
Maria Miguel Gomes
Carla Garcez
Filipa Leite
Tereza Oliva
António Santos
Armando Pinto
spellingShingle Cláudia Patraquim
Maria Miguel Gomes
Carla Garcez
Filipa Leite
Tereza Oliva
António Santos
Armando Pinto
Childhood Hypopigmented Mycosis Fungoides: A Rare Diagnosis
Case Reports in Pediatrics
author_facet Cláudia Patraquim
Maria Miguel Gomes
Carla Garcez
Filipa Leite
Tereza Oliva
António Santos
Armando Pinto
author_sort Cláudia Patraquim
title Childhood Hypopigmented Mycosis Fungoides: A Rare Diagnosis
title_short Childhood Hypopigmented Mycosis Fungoides: A Rare Diagnosis
title_full Childhood Hypopigmented Mycosis Fungoides: A Rare Diagnosis
title_fullStr Childhood Hypopigmented Mycosis Fungoides: A Rare Diagnosis
title_full_unstemmed Childhood Hypopigmented Mycosis Fungoides: A Rare Diagnosis
title_sort childhood hypopigmented mycosis fungoides: a rare diagnosis
publisher Hindawi Limited
series Case Reports in Pediatrics
issn 2090-6803
2090-6811
publishDate 2016-01-01
description Primary cutaneous lymphomas (PCL) are rare in pediatrics. Mycosis fungoides (MF) is the most frequent PCL diagnosed in childhood. There are various clinical variants of MF, including the hypopigmented MF (HMF). We present a 5-year-old boy with an 18-month history of progressive, generalized, nonpruritic hypopigmented lesions with central lacy erythema. He had no improvement with emollients. Skin biopsy showed typical features of HMF. He was treated with topical corticosteroids and tacrolimus and narrow-band ultraviolet B (NBUVB) phototherapy, with good response. HMF may mimic multiple skin disorders. Unusual hypopigmented skin lesions should be biopsied. Though phototherapy is effective, recurrence is common.
url http://dx.doi.org/10.1155/2016/8564389
work_keys_str_mv AT claudiapatraquim childhoodhypopigmentedmycosisfungoidesararediagnosis
AT mariamiguelgomes childhoodhypopigmentedmycosisfungoidesararediagnosis
AT carlagarcez childhoodhypopigmentedmycosisfungoidesararediagnosis
AT filipaleite childhoodhypopigmentedmycosisfungoidesararediagnosis
AT terezaoliva childhoodhypopigmentedmycosisfungoidesararediagnosis
AT antoniosantos childhoodhypopigmentedmycosisfungoidesararediagnosis
AT armandopinto childhoodhypopigmentedmycosisfungoidesararediagnosis
_version_ 1725324799419351040