Revisiting the question of pemphigus classification

• Main Authors: Alexey V. Samtsov, Evgeny V. Sokolovskiy, Natalia P. Teplyuk, Irena E. Belousova, Muza M. Kokhan, Elena V. Matushevskaya
• Format: Article
• Language: Russian
• Published: State Scientific Center of Dermatovenereology and Cosmetology 2021-04-01
• Series: Vestnik Dermatologii i Venerologii
• Subjects: pemphigus; classification; pathophysiology
• Online Access: https://vestnikdv.ru/jour/article/viewFile/1216/1186

Analysis of various classifications of pemphigus shows that there are no fundamental differences between them. The main distinctions consist in use of diverse terms in naming of some forms of pemphigus and in inclusion or exclusion of certain subtypes from the classifications. Authors propose to use the following classification in the dermatological clinical practice, for educational and scientific purposes and for clinical guidelines: 1) pemphigus vulgaris (1.1. Pemphigu s vegetans); 2) pemphigus foliaceus (2.1. Pemphigus endemic (Fogo selvagem), 2.2. Pemphigus erythematosus (Senear Usher)); 3) herpetiform pemphigus; 4) paraneoplastic pemphigus; 5) IgA pemphigus (5.1. Subcorneal pustular dermatosis, 5.2. Intraepidermal neutrophilic dermatosis).