Hughes-Stovin syndrome revealing the presence of Behçet’s Disease
Background: Hughes-Stovin Syndrome (HSS) is a rare clinical disorder characterized by deep venous thrombosis and multiple pulmonary and/or bronchial aneurysms. Aneurysms in systemic circulation can also be seen. Case presentation: We report the first case of HSS with aortic aneurysm in a 55-year-old...
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Babol University of Medical Sciences
2017-07-01
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doaj-b568ae80eeca4612b8a3afa8dc074fa32020-11-24T20:53:35ZengBabol University of Medical SciencesCaspian Journal of Internal Medicine2008-61642008-61722017-07-0184332334Hughes-Stovin syndrome revealing the presence of Behçet’s DiseaseMelek Kechida0Sondes Yaacoubi1Ahmed Zrig2Walid Jomaa3Rim Klii4Sonia Hammami5Ines Khochtali6 Department of Internal Medicine and Endocrinology, Fattouma Bourguiba Hospital, University of Monastir, Tunisia Department of Internal Medicine and Endocrinology, Fattouma Bourguiba Hospital, University of Monastir, Tunisia Department of Radiology, Fattouma Bourguiba Hospital, University of Monastir, Tunisia. Department of Cardiology, Fattouma Bourguiba Hospital, University of Monastir, Tunisia Department of Internal Medicine and Endocrinology, Fattouma Bourguiba Hospital, University of Monastir, Tunisia Department of Internal Medicine and Endocrinology, Fattouma Bourguiba Hospital, University of Monastir, Tunisia Department of Internal Medicine and Endocrinology, Fattouma Bourguiba Hospital, University of Monastir, Tunisia Background: Hughes-Stovin Syndrome (HSS) is a rare clinical disorder characterized by deep venous thrombosis and multiple pulmonary and/or bronchial aneurysms. Aneurysms in systemic circulation can also be seen. Case presentation: We report the first case of HSS with aortic aneurysm in a 55-year-old man who initially presented with deep venous thrombosis. The diagnosis of HSS revealing Behçet’s disease was made given the history of recurrent oral and genital ulcers. Treatment consisted of 3 daily pulses of methylprednisolone (1g) followed by oral prednisone (1mg/kg daily) and 6 monthly pulses of cyclophosphamide. Oral anticoagulation treatment was held 3 months and then was stopped with good outcome. Conclusion: Systemic aneurysms in Hughes Stovin is a worth knowing complication which may reveal Behçet’s disease.http://caspjim.com/browse.php?a_code=A-10-622-1&slc_lang=en&sid=1Behçet syndrome Hughes-Stovin syndrome Aortic aneurysm |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Melek Kechida Sondes Yaacoubi Ahmed Zrig Walid Jomaa Rim Klii Sonia Hammami Ines Khochtali |
spellingShingle |
Melek Kechida Sondes Yaacoubi Ahmed Zrig Walid Jomaa Rim Klii Sonia Hammami Ines Khochtali Hughes-Stovin syndrome revealing the presence of Behçet’s Disease Caspian Journal of Internal Medicine Behçet syndrome Hughes-Stovin syndrome Aortic aneurysm |
author_facet |
Melek Kechida Sondes Yaacoubi Ahmed Zrig Walid Jomaa Rim Klii Sonia Hammami Ines Khochtali |
author_sort |
Melek Kechida |
title |
Hughes-Stovin syndrome revealing the presence of Behçet’s Disease |
title_short |
Hughes-Stovin syndrome revealing the presence of Behçet’s Disease |
title_full |
Hughes-Stovin syndrome revealing the presence of Behçet’s Disease |
title_fullStr |
Hughes-Stovin syndrome revealing the presence of Behçet’s Disease |
title_full_unstemmed |
Hughes-Stovin syndrome revealing the presence of Behçet’s Disease |
title_sort |
hughes-stovin syndrome revealing the presence of behçet’s disease |
publisher |
Babol University of Medical Sciences |
series |
Caspian Journal of Internal Medicine |
issn |
2008-6164 2008-6172 |
publishDate |
2017-07-01 |
description |
Background: Hughes-Stovin Syndrome (HSS) is a rare clinical disorder characterized by deep venous thrombosis and multiple pulmonary and/or bronchial aneurysms. Aneurysms in systemic circulation can also be seen.
Case presentation: We report the first case of HSS with aortic aneurysm in a 55-year-old man who initially presented with deep venous thrombosis. The diagnosis of HSS revealing Behçet’s disease was made given the history of recurrent oral and genital ulcers. Treatment consisted of 3 daily pulses of methylprednisolone (1g) followed by oral prednisone (1mg/kg daily) and 6 monthly pulses of cyclophosphamide. Oral anticoagulation treatment was held 3 months and then was stopped with good outcome.
Conclusion: Systemic aneurysms in Hughes Stovin is a worth knowing complication which may reveal Behçet’s disease. |
topic |
Behçet syndrome Hughes-Stovin syndrome Aortic aneurysm |
url |
http://caspjim.com/browse.php?a_code=A-10-622-1&slc_lang=en&sid=1 |
work_keys_str_mv |
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1716796861401006080 |