Similarities of Variant Creutzfeldt-Jakob Disease Strain in Mother and Son in Spain to UK Reference Case

We investigated transmission characteristics of variant Creutzfeldt-Jakob disease in a mother and son from Spain. Despite differences in patient age and disease manifestations, we found the same strain properties in these patients as in UK vCJD cases. A single strain of agent appears to be responsib...

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Main Authors: Abigail B. Diack, Aileen Boyle, Diane Ritchie, Chris Plinston, Dorothy Kisielewski, Jesús de Pedro-Cuesta, Alberto Rábano, Robert G. Will, Jean C. Manson
Format: Article
Language:English
Published: Centers for Disease Control and Prevention 2017-09-01
Series:Emerging Infectious Diseases
Subjects:
BSE
Online Access:https://wwwnc.cdc.gov/eid/article/23/9/17-0159_article
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spelling doaj-b620a24940044c778625fd4f6dd6bdbf2020-11-25T00:38:19ZengCenters for Disease Control and PreventionEmerging Infectious Diseases1080-60401080-60592017-09-012391593159610.3201/eid2309.170159Similarities of Variant Creutzfeldt-Jakob Disease Strain in Mother and Son in Spain to UK Reference CaseAbigail B. DiackAileen BoyleDiane RitchieChris PlinstonDorothy KisielewskiJesús de Pedro-CuestaAlberto RábanoRobert G. WillJean C. MansonWe investigated transmission characteristics of variant Creutzfeldt-Jakob disease in a mother and son from Spain. Despite differences in patient age and disease manifestations, we found the same strain properties in these patients as in UK vCJD cases. A single strain of agent appears to be responsible for all vCJD cases to date.https://wwwnc.cdc.gov/eid/article/23/9/17-0159_articleprionstrainvariant Creutzfeldt-Jakob diseasevCJDBSEtransmissible spongiform encephalopathy
collection DOAJ
language English
format Article
sources DOAJ
author Abigail B. Diack
Aileen Boyle
Diane Ritchie
Chris Plinston
Dorothy Kisielewski
Jesús de Pedro-Cuesta
Alberto Rábano
Robert G. Will
Jean C. Manson
spellingShingle Abigail B. Diack
Aileen Boyle
Diane Ritchie
Chris Plinston
Dorothy Kisielewski
Jesús de Pedro-Cuesta
Alberto Rábano
Robert G. Will
Jean C. Manson
Similarities of Variant Creutzfeldt-Jakob Disease Strain in Mother and Son in Spain to UK Reference Case
Emerging Infectious Diseases
prion
strain
variant Creutzfeldt-Jakob disease
vCJD
BSE
transmissible spongiform encephalopathy
author_facet Abigail B. Diack
Aileen Boyle
Diane Ritchie
Chris Plinston
Dorothy Kisielewski
Jesús de Pedro-Cuesta
Alberto Rábano
Robert G. Will
Jean C. Manson
author_sort Abigail B. Diack
title Similarities of Variant Creutzfeldt-Jakob Disease Strain in Mother and Son in Spain to UK Reference Case
title_short Similarities of Variant Creutzfeldt-Jakob Disease Strain in Mother and Son in Spain to UK Reference Case
title_full Similarities of Variant Creutzfeldt-Jakob Disease Strain in Mother and Son in Spain to UK Reference Case
title_fullStr Similarities of Variant Creutzfeldt-Jakob Disease Strain in Mother and Son in Spain to UK Reference Case
title_full_unstemmed Similarities of Variant Creutzfeldt-Jakob Disease Strain in Mother and Son in Spain to UK Reference Case
title_sort similarities of variant creutzfeldt-jakob disease strain in mother and son in spain to uk reference case
publisher Centers for Disease Control and Prevention
series Emerging Infectious Diseases
issn 1080-6040
1080-6059
publishDate 2017-09-01
description We investigated transmission characteristics of variant Creutzfeldt-Jakob disease in a mother and son from Spain. Despite differences in patient age and disease manifestations, we found the same strain properties in these patients as in UK vCJD cases. A single strain of agent appears to be responsible for all vCJD cases to date.
topic prion
strain
variant Creutzfeldt-Jakob disease
vCJD
BSE
transmissible spongiform encephalopathy
url https://wwwnc.cdc.gov/eid/article/23/9/17-0159_article
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