Isolated double chambered right ventricle as a rare cause of sudden death in infancy

Isolated double-chambered right ventricle (DCRV) is a rare form of congenital heart disorder in which the right ventricle is divided into a high-pressure inlet portion and a low-pressure outlet portion by an anomalous muscle bundle. Rarely, autopsy cases describing this congenital heart disease have...

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Bibliographic Details
Main Authors: W. Thaljawi, M. Belhadj, Y. Chkirben, S. Bouslema, M. Jedidi, T. Masmoudi, M.K Souguir, M.T. Yaâcoubi, M. Ben Dhiab
Format: Article
Language:English
Published: SpringerOpen 2016-12-01
Series:Egyptian Journal of Forensic Sciences
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Online Access:http://www.sciencedirect.com/science/article/pii/S2090536X16300090
Description
Summary:Isolated double-chambered right ventricle (DCRV) is a rare form of congenital heart disorder in which the right ventricle is divided into a high-pressure inlet portion and a low-pressure outlet portion by an anomalous muscle bundle. Rarely, autopsy cases describing this congenital heart disease have been reported in the world literature. We report the case of a 50-day-old male who died seven days after been suffering from fever and dyspnea. The autopsy revealed essentially an isolated double-chambered right ventricle (DCRV) and an important pulmonary edema. In this paper, we present the first reported case of sudden unanticipated death in infancy due to isolated double-chambered right ventricle.
ISSN:2090-536X