Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome

Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome

Sturge–Weber syndrome (SWS) is a rare neuro-oculocutaneous disorder. The classical signs are unilateral facial port wine stain, leptomeningeal angiomas, and their sequele with ipsilateral glaucoma. Here, we are reporting two cases of SWS associated with conjunctival melanosis and retinal vascular to...

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Bibliographic Details
Main Authors: Padma B Prabhu, Deviprasad Soman, V Babitha
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2017-01-01
Series:Kerala Journal of Ophthalmology
Subjects:
Conjunctival melanosis
leptomeningeal angioma
phacomatosis pigmentovascularis
port wine stain
retinal vessel tortuosity
Sturge–Weber syndrome
Online Access:http://www.kjophthal.com/article.asp?issn=0976-6677;year=2017;volume=29;issue=3;spage=226;epage=229;aulast=Prabhu
Description
Summary:Sturge–Weber syndrome (SWS) is a rare neuro-oculocutaneous disorder. The classical signs are unilateral facial port wine stain, leptomeningeal angiomas, and their sequele with ipsilateral glaucoma. Here, we are reporting two cases of SWS associated with conjunctival melanosis and retinal vascular tortuosity. This unusual coincidence maybe representative of a unique entity named phacomatosis pigmentovascularis.
ISSN:0976-6677

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