Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome

Sturge–Weber syndrome (SWS) is a rare neuro-oculocutaneous disorder. The classical signs are unilateral facial port wine stain, leptomeningeal angiomas, and their sequele with ipsilateral glaucoma. Here, we are reporting two cases of SWS associated with conjunctival melanosis and retinal vascular to...

Full description

Bibliographic Details
Main Authors: Padma B Prabhu, Deviprasad Soman, V Babitha
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2017-01-01
Series:Kerala Journal of Ophthalmology
Subjects:
Online Access:http://www.kjophthal.com/article.asp?issn=0976-6677;year=2017;volume=29;issue=3;spage=226;epage=229;aulast=Prabhu
id doaj-b872e5213747408cb6875f0fe01143dc
record_format Article
spelling doaj-b872e5213747408cb6875f0fe01143dc2020-11-24T21:11:10ZengWolters Kluwer Medknow PublicationsKerala Journal of Ophthalmology0976-66772017-01-0129322622910.4103/kjo.kjo_95_17Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndromePadma B PrabhuDeviprasad SomanV BabithaSturge–Weber syndrome (SWS) is a rare neuro-oculocutaneous disorder. The classical signs are unilateral facial port wine stain, leptomeningeal angiomas, and their sequele with ipsilateral glaucoma. Here, we are reporting two cases of SWS associated with conjunctival melanosis and retinal vascular tortuosity. This unusual coincidence maybe representative of a unique entity named phacomatosis pigmentovascularis.http://www.kjophthal.com/article.asp?issn=0976-6677;year=2017;volume=29;issue=3;spage=226;epage=229;aulast=PrabhuConjunctival melanosisleptomeningeal angiomaphacomatosis pigmentovascularisport wine stainretinal vessel tortuositySturge–Weber syndrome
collection DOAJ
language English
format Article
sources DOAJ
author Padma B Prabhu
Deviprasad Soman
V Babitha
spellingShingle Padma B Prabhu
Deviprasad Soman
V Babitha
Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome
Kerala Journal of Ophthalmology
Conjunctival melanosis
leptomeningeal angioma
phacomatosis pigmentovascularis
port wine stain
retinal vessel tortuosity
Sturge–Weber syndrome
author_facet Padma B Prabhu
Deviprasad Soman
V Babitha
author_sort Padma B Prabhu
title Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome
title_short Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome
title_full Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome
title_fullStr Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome
title_full_unstemmed Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome
title_sort conjunctival melanosis with retinal vessel tortuosity: an unusual presentation of sturge–weber syndrome
publisher Wolters Kluwer Medknow Publications
series Kerala Journal of Ophthalmology
issn 0976-6677
publishDate 2017-01-01
description Sturge–Weber syndrome (SWS) is a rare neuro-oculocutaneous disorder. The classical signs are unilateral facial port wine stain, leptomeningeal angiomas, and their sequele with ipsilateral glaucoma. Here, we are reporting two cases of SWS associated with conjunctival melanosis and retinal vascular tortuosity. This unusual coincidence maybe representative of a unique entity named phacomatosis pigmentovascularis.
topic Conjunctival melanosis
leptomeningeal angioma
phacomatosis pigmentovascularis
port wine stain
retinal vessel tortuosity
Sturge–Weber syndrome
url http://www.kjophthal.com/article.asp?issn=0976-6677;year=2017;volume=29;issue=3;spage=226;epage=229;aulast=Prabhu
work_keys_str_mv AT padmabprabhu conjunctivalmelanosiswithretinalvesseltortuosityanunusualpresentationofsturgewebersyndrome
AT deviprasadsoman conjunctivalmelanosiswithretinalvesseltortuosityanunusualpresentationofsturgewebersyndrome
AT vbabitha conjunctivalmelanosiswithretinalvesseltortuosityanunusualpresentationofsturgewebersyndrome
_version_ 1716754237786947584