Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome
Sturge–Weber syndrome (SWS) is a rare neuro-oculocutaneous disorder. The classical signs are unilateral facial port wine stain, leptomeningeal angiomas, and their sequele with ipsilateral glaucoma. Here, we are reporting two cases of SWS associated with conjunctival melanosis and retinal vascular to...
Main Authors: | , , |
---|---|
Format: | Article |
Language: | English |
Published: |
Wolters Kluwer Medknow Publications
2017-01-01
|
Series: | Kerala Journal of Ophthalmology |
Subjects: | |
Online Access: | http://www.kjophthal.com/article.asp?issn=0976-6677;year=2017;volume=29;issue=3;spage=226;epage=229;aulast=Prabhu |
id |
doaj-b872e5213747408cb6875f0fe01143dc |
---|---|
record_format |
Article |
spelling |
doaj-b872e5213747408cb6875f0fe01143dc2020-11-24T21:11:10ZengWolters Kluwer Medknow PublicationsKerala Journal of Ophthalmology0976-66772017-01-0129322622910.4103/kjo.kjo_95_17Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndromePadma B PrabhuDeviprasad SomanV BabithaSturge–Weber syndrome (SWS) is a rare neuro-oculocutaneous disorder. The classical signs are unilateral facial port wine stain, leptomeningeal angiomas, and their sequele with ipsilateral glaucoma. Here, we are reporting two cases of SWS associated with conjunctival melanosis and retinal vascular tortuosity. This unusual coincidence maybe representative of a unique entity named phacomatosis pigmentovascularis.http://www.kjophthal.com/article.asp?issn=0976-6677;year=2017;volume=29;issue=3;spage=226;epage=229;aulast=PrabhuConjunctival melanosisleptomeningeal angiomaphacomatosis pigmentovascularisport wine stainretinal vessel tortuositySturge–Weber syndrome |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Padma B Prabhu Deviprasad Soman V Babitha |
spellingShingle |
Padma B Prabhu Deviprasad Soman V Babitha Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome Kerala Journal of Ophthalmology Conjunctival melanosis leptomeningeal angioma phacomatosis pigmentovascularis port wine stain retinal vessel tortuosity Sturge–Weber syndrome |
author_facet |
Padma B Prabhu Deviprasad Soman V Babitha |
author_sort |
Padma B Prabhu |
title |
Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome |
title_short |
Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome |
title_full |
Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome |
title_fullStr |
Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome |
title_full_unstemmed |
Conjunctival melanosis with retinal vessel tortuosity: An unusual presentation of Sturge–Weber syndrome |
title_sort |
conjunctival melanosis with retinal vessel tortuosity: an unusual presentation of sturge–weber syndrome |
publisher |
Wolters Kluwer Medknow Publications |
series |
Kerala Journal of Ophthalmology |
issn |
0976-6677 |
publishDate |
2017-01-01 |
description |
Sturge–Weber syndrome (SWS) is a rare neuro-oculocutaneous disorder. The classical signs are unilateral facial port wine stain, leptomeningeal angiomas, and their sequele with ipsilateral glaucoma. Here, we are reporting two cases of SWS associated with conjunctival melanosis and retinal vascular tortuosity. This unusual coincidence maybe representative of a unique entity named phacomatosis pigmentovascularis. |
topic |
Conjunctival melanosis leptomeningeal angioma phacomatosis pigmentovascularis port wine stain retinal vessel tortuosity Sturge–Weber syndrome |
url |
http://www.kjophthal.com/article.asp?issn=0976-6677;year=2017;volume=29;issue=3;spage=226;epage=229;aulast=Prabhu |
work_keys_str_mv |
AT padmabprabhu conjunctivalmelanosiswithretinalvesseltortuosityanunusualpresentationofsturgewebersyndrome AT deviprasadsoman conjunctivalmelanosiswithretinalvesseltortuosityanunusualpresentationofsturgewebersyndrome AT vbabitha conjunctivalmelanosiswithretinalvesseltortuosityanunusualpresentationofsturgewebersyndrome |
_version_ |
1716754237786947584 |