Low-grade myofibroblastic sarcoma: a case report of a child

• Main Authors: Hamon Julien, Bourkis Amélie, Le Toux Guy
• Format: Article
• Language: English
• Published: EDP Sciences 2019-01-01
• Series: Journal of Oral Medicine and Oral Surgery
• Subjects: sarcoma; myofibroblaste; mouth
• Online Access: https://www.jomos.org/articles/mbcb/full_html/2019/03/mbcb190004/mbcb190004.html

Introduction: Myofibroblastic sarcomas are malignant tumors characterized by the increased proliferation of myofibroblasts; they are rare and have been recently discovered. Observation: A 14-year-old adolescent had a large lesion in the inside of her right mandible. The diagnosis, after a difficult histological analysis, was low-grade myofibrosarcoma. The patient was treated with non-interruptive hemimandibulectomy. Discussion: Low-grade myofibroblastic sarcoma is one of four types of myofibroblastic sarcomas recognized by the WHO in the 2001 classification. This classification allows us to determine a prognosis based on histological characteristics of the lesion. Conclusion: In all cases of low-grade myofibroblastic sarcoma, the preferred treatment is curative surgical resection; but still poses a problem in the prosthetic rehabilitation of oral lesion.