Primary extrauterine cystic low-grade endometrioid stromal sarcoma mimicking stromal endometriosis. A case report emphasizing the differential diagnosis and its potential local aggressive behavior

• Main Authors: Simona Stolnicu, Csilip Tunde, Gabos Szilard, Cristian Podoleanu, Francisc Rozsnyai
• Format: Article
• Language: English
• Published: Termedia Publishing House 2020-10-01
• Series: Polish Journal of Pathology
• Subjects: stromal endometriosis; cystic endometrial stromal sarcoma; malignant transformation
• Online Access: https://www.termedia.pl/Primary-extrauterine-cystic-low-grade-endometrioid-stromal-sarcoma-mimicking-stromal-endometriosis-A-case-report-emphasizing-the-differential-diagnosis-and-its-potential-local-aggressive-behavior,55,42029,1,1.html

Genital and pelvic endometriosis is a frequently encountered lesion and its importance rely on associated symptoms and its propensity for malignant transformation. In the present paper we comment on the importance of correctly diagnose the malignant transformation of an endometriotic lesion into a cystic low-grade endometrial stromal sarcoma, which is a very rare event. Moreover, we discuss the ability of a low-grade endometrial stromal sarcoma to locally recurr and the differential diagnosis with stromal endometriosis, a lesion that is very rare, almost always microscopic and solid.