A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation

A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation

Cor triatriatum sinister is a rare congenital cardiac anomaly. The anomaly is caused by a fibromuscular membrane that divides the left atrium into two cavities. This membrane can lead to the obstruction of left atrial flow and also create pulmonary venous hypertension. Pulmonary arteriovenous malfor...

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Main Authors: Can Yilmaz Yozgat, Erkan Cakir, Hakan Yazan, Hafize Otcu Temur, Kahraman Yakut, Yilmaz Yozgat
Format: Article
Language:English
Published: Hindawi Limited 2020-01-01
Series:Case Reports in Pediatrics
Online Access:http://dx.doi.org/10.1155/2020/8825215
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spelling doaj-bea978f931f8475dbab5dd8aeb9b63f62020-11-25T04:12:27ZengHindawi LimitedCase Reports in Pediatrics2090-68032090-68112020-01-01202010.1155/2020/88252158825215A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous MalformationCan Yilmaz Yozgat0Erkan Cakir1Hakan Yazan2Hafize Otcu Temur3Kahraman Yakut4Yilmaz Yozgat5Faculty of Medicine, Bezmialem Vakif University, Istanbul, TurkeyDepartment of Pediatric Pulmonology, Bezmialem Vakif University, Istanbul, TurkeyDepartment of Pediatric Pulmonology, Bezmialem Vakif University, Istanbul, TurkeyDepartment of Radiology, Bezmialem Vakif University, Istanbul, TurkeyDepartment of Pediatric Cardiology, Bezmialem Vakif University, Istanbul, TurkeyDepartment of Pediatric Cardiology, Bezmialem Vakif University, Istanbul, TurkeyCor triatriatum sinister is a rare congenital cardiac anomaly. The anomaly is caused by a fibromuscular membrane that divides the left atrium into two cavities. This membrane can lead to the obstruction of left atrial flow and also create pulmonary venous hypertension. Pulmonary arteriovenous malformation (PAVM) is notorious for its aberrant blood flow between the pulmonary arteries and veins. Herein, we report a case of a 4-year-old toddler who had a unique form of pulmonary hypertension presenting with cor triatriatum sinister and diffuse PAVM. After the surgical treatment of cor triatriatum sinister, both pulmonary arteriovenous malformation and pulmonary hypertension disappeared.http://dx.doi.org/10.1155/2020/8825215
collection DOAJ
language English
format Article
sources DOAJ
author Can Yilmaz Yozgat
Erkan Cakir
Hakan Yazan
Hafize Otcu Temur
Kahraman Yakut
Yilmaz Yozgat
spellingShingle Can Yilmaz Yozgat
Erkan Cakir
Hakan Yazan
Hafize Otcu Temur
Kahraman Yakut
Yilmaz Yozgat
A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation
Case Reports in Pediatrics
author_facet Can Yilmaz Yozgat
Erkan Cakir
Hakan Yazan
Hafize Otcu Temur
Kahraman Yakut
Yilmaz Yozgat
author_sort Can Yilmaz Yozgat
title A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation
title_short A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation
title_full A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation
title_fullStr A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation
title_full_unstemmed A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation
title_sort rare cause of pulmonary hypertension in a 4-year-old toddler: association of cor triatriatum sinister and pulmonary arteriovenous malformation
publisher Hindawi Limited
series Case Reports in Pediatrics
issn 2090-6803
2090-6811
publishDate 2020-01-01
description Cor triatriatum sinister is a rare congenital cardiac anomaly. The anomaly is caused by a fibromuscular membrane that divides the left atrium into two cavities. This membrane can lead to the obstruction of left atrial flow and also create pulmonary venous hypertension. Pulmonary arteriovenous malformation (PAVM) is notorious for its aberrant blood flow between the pulmonary arteries and veins. Herein, we report a case of a 4-year-old toddler who had a unique form of pulmonary hypertension presenting with cor triatriatum sinister and diffuse PAVM. After the surgical treatment of cor triatriatum sinister, both pulmonary arteriovenous malformation and pulmonary hypertension disappeared.
url http://dx.doi.org/10.1155/2020/8825215
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