A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation
Cor triatriatum sinister is a rare congenital cardiac anomaly. The anomaly is caused by a fibromuscular membrane that divides the left atrium into two cavities. This membrane can lead to the obstruction of left atrial flow and also create pulmonary venous hypertension. Pulmonary arteriovenous malfor...
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2020-01-01
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Series: | Case Reports in Pediatrics |
Online Access: | http://dx.doi.org/10.1155/2020/8825215 |
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doaj-bea978f931f8475dbab5dd8aeb9b63f62020-11-25T04:12:27ZengHindawi LimitedCase Reports in Pediatrics2090-68032090-68112020-01-01202010.1155/2020/88252158825215A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous MalformationCan Yilmaz Yozgat0Erkan Cakir1Hakan Yazan2Hafize Otcu Temur3Kahraman Yakut4Yilmaz Yozgat5Faculty of Medicine, Bezmialem Vakif University, Istanbul, TurkeyDepartment of Pediatric Pulmonology, Bezmialem Vakif University, Istanbul, TurkeyDepartment of Pediatric Pulmonology, Bezmialem Vakif University, Istanbul, TurkeyDepartment of Radiology, Bezmialem Vakif University, Istanbul, TurkeyDepartment of Pediatric Cardiology, Bezmialem Vakif University, Istanbul, TurkeyDepartment of Pediatric Cardiology, Bezmialem Vakif University, Istanbul, TurkeyCor triatriatum sinister is a rare congenital cardiac anomaly. The anomaly is caused by a fibromuscular membrane that divides the left atrium into two cavities. This membrane can lead to the obstruction of left atrial flow and also create pulmonary venous hypertension. Pulmonary arteriovenous malformation (PAVM) is notorious for its aberrant blood flow between the pulmonary arteries and veins. Herein, we report a case of a 4-year-old toddler who had a unique form of pulmonary hypertension presenting with cor triatriatum sinister and diffuse PAVM. After the surgical treatment of cor triatriatum sinister, both pulmonary arteriovenous malformation and pulmonary hypertension disappeared.http://dx.doi.org/10.1155/2020/8825215 |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Can Yilmaz Yozgat Erkan Cakir Hakan Yazan Hafize Otcu Temur Kahraman Yakut Yilmaz Yozgat |
spellingShingle |
Can Yilmaz Yozgat Erkan Cakir Hakan Yazan Hafize Otcu Temur Kahraman Yakut Yilmaz Yozgat A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation Case Reports in Pediatrics |
author_facet |
Can Yilmaz Yozgat Erkan Cakir Hakan Yazan Hafize Otcu Temur Kahraman Yakut Yilmaz Yozgat |
author_sort |
Can Yilmaz Yozgat |
title |
A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation |
title_short |
A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation |
title_full |
A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation |
title_fullStr |
A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation |
title_full_unstemmed |
A Rare Cause of Pulmonary Hypertension in a 4-Year-Old Toddler: Association of Cor Triatriatum Sinister and Pulmonary Arteriovenous Malformation |
title_sort |
rare cause of pulmonary hypertension in a 4-year-old toddler: association of cor triatriatum sinister and pulmonary arteriovenous malformation |
publisher |
Hindawi Limited |
series |
Case Reports in Pediatrics |
issn |
2090-6803 2090-6811 |
publishDate |
2020-01-01 |
description |
Cor triatriatum sinister is a rare congenital cardiac anomaly. The anomaly is caused by a fibromuscular membrane that divides the left atrium into two cavities. This membrane can lead to the obstruction of left atrial flow and also create pulmonary venous hypertension. Pulmonary arteriovenous malformation (PAVM) is notorious for its aberrant blood flow between the pulmonary arteries and veins. Herein, we report a case of a 4-year-old toddler who had a unique form of pulmonary hypertension presenting with cor triatriatum sinister and diffuse PAVM. After the surgical treatment of cor triatriatum sinister, both pulmonary arteriovenous malformation and pulmonary hypertension disappeared. |
url |
http://dx.doi.org/10.1155/2020/8825215 |
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