A Rare Case of Hyper IgE Syndrome with Vocal Cords Involvement

Hyperimmunoglobulin E syndrome (HIGE) is considered as a phagocytic or a newly classified complex and heterogeneous primary immunodeficiency disease with symptoms such as increased levels of immunoglobulin E, eczema, and, recurrent lung and skin infections. In this paper, we have presented a rare c...

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Main Authors:	Samin Sharafian, Masoud Movahedi, Arash Kalantari, Nima Parvaneh, Mohammad Gharagozlou
Format:	Article
Language:	English
Published:	Tehran University of Medical Sciences 2019-04-01
Series:	Iranian Journal of Allergy, Asthma and Immunology
Subjects:	Cauliflower Hyperimmunoglobulin E syndrome Immunodeficiency Lesions
Online Access:	https://ijaai.tums.ac.ir/index.php/ijaai/article/view/1836

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spelling	doaj-c4198bb2cb6b4b0fbe8897dbd953d79c2020-11-25T04:12:30ZengTehran University of Medical SciencesIranian Journal of Allergy, Asthma and Immunology1735-15021735-52492019-04-0118210.18502/ijaai.v18i2.9261836A Rare Case of Hyper IgE Syndrome with Vocal Cords InvolvementSamin Sharafian0Masoud Movahedi1Arash Kalantari2Nima Parvaneh3Mohammad Gharagozlou4Department of Allergy and Clinical Immunology, School of Medicine, Bushehr University of Medical Sciences, Bushehr, IranDepartment of Allergy and Clinical Immunology, Children’s Medical Center, Tehran University of Medical Sciences, Tehran, IranDepartment of Allergy and Clinical Immunology, Vali-e-Asr Hospital, Imam Khomeini Hospital Complexes, Tehran University of Medical Sciences, Tehran, IranDepartment of Allergy and Clinical Immunology, Children’s Medical Center, Tehran University of Medical Sciences, Tehran, IranDepartment of Allergy and Clinical Immunology, Children’s Medical Center, Tehran University of Medical Sciences, Tehran, Iran Hyperimmunoglobulin E syndrome (HIGE) is considered as a phagocytic or a newly classified complex and heterogeneous primary immunodeficiency disease with symptoms such as increased levels of immunoglobulin E, eczema, and, recurrent lung and skin infections. In this paper, we have presented a rare case of this syndrome. A 9-year-old Iranian girl presented with a history of pruritic maculopapular rash who was eventually diagnosed as a case of HIGE. In her recent admission, she had dysphonia, stridor and huge cauliflower cutaneous lesions on her neck, finger and vocal cords, which did not respond to intravenous antibiotics, and ultimately required surgical removal. https://ijaai.tums.ac.ir/index.php/ijaai/article/view/1836CauliflowerHyperimmunoglobulin E syndromeImmunodeficiencyLesions
collection	DOAJ
language	English
format	Article
sources	DOAJ
author	Samin Sharafian Masoud Movahedi Arash Kalantari Nima Parvaneh Mohammad Gharagozlou
spellingShingle	Samin Sharafian Masoud Movahedi Arash Kalantari Nima Parvaneh Mohammad Gharagozlou A Rare Case of Hyper IgE Syndrome with Vocal Cords Involvement Iranian Journal of Allergy, Asthma and Immunology Cauliflower Hyperimmunoglobulin E syndrome Immunodeficiency Lesions
author_facet	Samin Sharafian Masoud Movahedi Arash Kalantari Nima Parvaneh Mohammad Gharagozlou
author_sort	Samin Sharafian
title	A Rare Case of Hyper IgE Syndrome with Vocal Cords Involvement
title_short	A Rare Case of Hyper IgE Syndrome with Vocal Cords Involvement
title_full	A Rare Case of Hyper IgE Syndrome with Vocal Cords Involvement
title_fullStr	A Rare Case of Hyper IgE Syndrome with Vocal Cords Involvement
title_full_unstemmed	A Rare Case of Hyper IgE Syndrome with Vocal Cords Involvement
title_sort	rare case of hyper ige syndrome with vocal cords involvement
publisher	Tehran University of Medical Sciences
series	Iranian Journal of Allergy, Asthma and Immunology
issn	1735-1502 1735-5249
publishDate	2019-04-01
description	Hyperimmunoglobulin E syndrome (HIGE) is considered as a phagocytic or a newly classified complex and heterogeneous primary immunodeficiency disease with symptoms such as increased levels of immunoglobulin E, eczema, and, recurrent lung and skin infections. In this paper, we have presented a rare case of this syndrome. A 9-year-old Iranian girl presented with a history of pruritic maculopapular rash who was eventually diagnosed as a case of HIGE. In her recent admission, she had dysphonia, stridor and huge cauliflower cutaneous lesions on her neck, finger and vocal cords, which did not respond to intravenous antibiotics, and ultimately required surgical removal.
topic	Cauliflower Hyperimmunoglobulin E syndrome Immunodeficiency Lesions
url	https://ijaai.tums.ac.ir/index.php/ijaai/article/view/1836
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A Rare Case of Hyper IgE Syndrome with Vocal Cords Involvement

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