Herlyn–Werner–Wünderlich syndrome: An unusual case with presentation of menorrhagia

Objective: Herlyn–Werner–Wünderlich (HWW) syndrome is a rare condition in which patients present with a palpable pelvic mass and pain caused by an obstructed hemivagina. Here we present a case of HWW syndrome characterized by prolonged menstrual bleeding. Case report: A 19-year-old nonsexually activ...

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Bibliographic Details
Main Authors: Hsin-I Liang, Shao-Chi Fu, Chih-Hsiang Yin, Cheng-Chang Chang
Format: Article
Language:English
Published: Elsevier 2020-11-01
Series:Taiwanese Journal of Obstetrics & Gynecology
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Online Access:http://www.sciencedirect.com/science/article/pii/S1028455920302370
Description
Summary:Objective: Herlyn–Werner–Wünderlich (HWW) syndrome is a rare condition in which patients present with a palpable pelvic mass and pain caused by an obstructed hemivagina. Here we present a case of HWW syndrome characterized by prolonged menstrual bleeding. Case report: A 19-year-old nonsexually active unmarried women experienced irregular menstrual cycles and menorrhagia. The duration of menstrual bleeding was 10–14 days. She also suffered from mild dysmenorrhea since menarche at the age of 13. Transabdominal sonography revealed a double uterus and a heterogeneous myoma-mimicking mass over the left cervical region. The left kidney was absent. Magnetic resonance imaging revealed a double uterus, a double vagina with an unperforated left hemivagina, and ipsilateral renal agenesis. The patient underwent cervicovaginal orifice reconstruction surgery. Conclusion: Left hematocolpos compression, a partially obstructed right vaginal channel, and an orifice with local venous drainage abnormalities resulted in prolonged menstrual bleeding. In HWW syndrome, the occurrence of a pelvic mass and pain is common; however, prolonged menstrual bleeding is rare.
ISSN:1028-4559