Acute pancreatitis caused by a duodenal duplication cyst covering the ampulla of Vater

• Main Authors: Katsuhiro Ogawa, Yutaka Kanamori, Toshihiko Watanabe, Kotaro Tomonaga, Mai Kutsukake, Michiko Goto, Michinobu Ohno, Kazunori Tahara, Tomoro Hishiki, Akihiro Fujino
• Format: Article
• Language: English
• Published: Elsevier 2018-07-01
• Series: Journal of Pediatric Surgery Case Reports
• Subjects: Duodenal duplication cyst; Duodenal atresia; Ampulla of Vater
• Online Access: http://www.sciencedirect.com/science/article/pii/S221357661830099X
• ISSN: 2213-5766

Duodenal duplication cyst is not a common congenital anomaly and the pathophysiology may become very complicated if the cyst is situated at the ampulla of Vater. Here we report a very rare female case of duodenal duplication cyst at the ampulla of Vater, which caused acute pancreatitis due to massive protein plaques in the pancreatic duct. She had a past history of double duodenal atresia and underwent surgery as a neonate. The correct diagnosis could not be determined before the second operation at four years of age and the exact pathophysiology finally became apparent during the operation with a contrast medium study and duodenotomy. We discuss the complicated clinical features and diagnostic and treatment procedures before and during the operation.