Abdominal Aggressive Fibromatosis: Diagnostic and Therapeutic Features
Desmoid tumours are rare soft tissue tumours developed from myofibroblasts. They usually infiltrate into adjacent muscle bundles and are characterised by the absence of metastatic potential. However, a high local aggressiveness is seen with a high rate of recurrence after surgical excision. We hereb...
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doaj-c99b126f3aa449ccba5a0a02b0b8d61e2020-11-25T03:54:37ZengJCDR Research and Publications Private LimitedJournal of Clinical and Diagnostic Research2249-782X0973-709X2018-04-01124XR01XR0310.7860/JCDR/2018/32311.11420Abdominal Aggressive Fibromatosis: Diagnostic and Therapeutic FeaturesHoucine Maghrebi0Amine Makni1Amine Sebai2Asma Labidi3Feriel Ksantini4Mohamed Jouini5Montassar Kacem6Zoubeir Bensafta7Associate Professor, Department of Surgery, Rabta Hospital, Tunis, Tunisia.Professor, Department of Surgery, Rabta Hospital, Tunis, Tunisia.Student, Department of Surgery, Rabta Hospital, Tunis, Tunisia.Associate Professor, Department of Gastroenterology, Rabta Hospital, Tunis, Tunisia.Associate Professor, Department of Surgery, Salah Azaiez Institute, Tunis, Tunisia.Professor, Department of Surgery, Rabta Hospital, Tunis, Tunisia.Professor, Department of Surgery, Rabta Hospital, Tunis, Tunisia.Professor, Department of Surgery, Rabta Hospital, Tunis, Tunisia.Desmoid tumours are rare soft tissue tumours developed from myofibroblasts. They usually infiltrate into adjacent muscle bundles and are characterised by the absence of metastatic potential. However, a high local aggressiveness is seen with a high rate of recurrence after surgical excision. We hereby attempt to present a series of patients with desmoid tumours and review treatment options and management strategies. Ten tumours occurred in the abdominal wall, five in the mesentery, and one was presacral tumour. The mean diameter of the tumour was 6 cm (range, 2.3-40 cm). Associated Familial Adenomatous Polyposis (FAP) was found in five patients. The margin of surgical resection was healthy in five patients. During follow up period, two patients returned with recurrence of tumours. https://jcdr.net/articles/PDF/11420/32311_F(SHU)_PF1(EK_SL)_PFA(EK_SL)_PB(EK_SL)_PN(SL).pdfdesmoid tumoursoncologysurgery |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
Houcine Maghrebi Amine Makni Amine Sebai Asma Labidi Feriel Ksantini Mohamed Jouini Montassar Kacem Zoubeir Bensafta |
spellingShingle |
Houcine Maghrebi Amine Makni Amine Sebai Asma Labidi Feriel Ksantini Mohamed Jouini Montassar Kacem Zoubeir Bensafta Abdominal Aggressive Fibromatosis: Diagnostic and Therapeutic Features Journal of Clinical and Diagnostic Research desmoid tumours oncology surgery |
author_facet |
Houcine Maghrebi Amine Makni Amine Sebai Asma Labidi Feriel Ksantini Mohamed Jouini Montassar Kacem Zoubeir Bensafta |
author_sort |
Houcine Maghrebi |
title |
Abdominal Aggressive Fibromatosis: Diagnostic and Therapeutic Features |
title_short |
Abdominal Aggressive Fibromatosis: Diagnostic and Therapeutic Features |
title_full |
Abdominal Aggressive Fibromatosis: Diagnostic and Therapeutic Features |
title_fullStr |
Abdominal Aggressive Fibromatosis: Diagnostic and Therapeutic Features |
title_full_unstemmed |
Abdominal Aggressive Fibromatosis: Diagnostic and Therapeutic Features |
title_sort |
abdominal aggressive fibromatosis: diagnostic and therapeutic features |
publisher |
JCDR Research and Publications Private Limited |
series |
Journal of Clinical and Diagnostic Research |
issn |
2249-782X 0973-709X |
publishDate |
2018-04-01 |
description |
Desmoid tumours are rare soft tissue tumours developed from myofibroblasts. They usually infiltrate into adjacent muscle bundles and are characterised by the absence of metastatic potential. However, a high local aggressiveness is seen with a high rate of recurrence after surgical excision. We hereby attempt to present a series of patients with desmoid tumours and review treatment options and management strategies. Ten tumours occurred in the abdominal wall, five in the mesentery, and one was presacral tumour. The mean diameter of the tumour was 6 cm (range, 2.3-40 cm). Associated Familial Adenomatous Polyposis (FAP) was found in five patients. The margin of surgical resection was healthy in five patients. During follow up period, two patients returned with recurrence of tumours. |
topic |
desmoid tumours oncology surgery |
url |
https://jcdr.net/articles/PDF/11420/32311_F(SHU)_PF1(EK_SL)_PFA(EK_SL)_PB(EK_SL)_PN(SL).pdf |
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