Craniotomy in Klippel-Trenaunay syndrome: Concerns and challenges
Klippel-Trenaunay syndrome (KTS) is a rare congenital disorder characterised by cutaneous capillary malformations, soft tissue and bone hypertrophy and venous varicosities. The coexistence of Chiari 1 malformation and an intracranial tumour has been rarely reported in the literature. Multisystem inv...
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doaj-cae808916b1a48be82bae777151a6c352020-11-25T02:04:09ZengWolters Kluwer Medknow PublicationsIndian Journal of Anaesthesia0019-50490976-28172019-01-0163121033103510.4103/ija.IJA_510_19Craniotomy in Klippel-Trenaunay syndrome: Concerns and challengesR P SangeethaNisha BaskarSriganesh KamathPriyadharshi DixitKlippel-Trenaunay syndrome (KTS) is a rare congenital disorder characterised by cutaneous capillary malformations, soft tissue and bone hypertrophy and venous varicosities. The coexistence of Chiari 1 malformation and an intracranial tumour has been rarely reported in the literature. Multisystem involvement of this syndrome mandates adequate preparation and planning, with meticulous conduct of anaesthesia to achieve favourable outcomes. We report a case of KTS syndrome with Chiari 1 malformation who had presented for craniotomy, and thereby discuss the challenges faced during anaesthetic management of these patients for major surgeries.http://www.ijaweb.org/article.asp?issn=0019-5049;year=2019;volume=63;issue=12;spage=1033;epage=1035;aulast=Sangeethachiari malformationklippel-trenaunay syndromeneurosurgery |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
R P Sangeetha Nisha Baskar Sriganesh Kamath Priyadharshi Dixit |
spellingShingle |
R P Sangeetha Nisha Baskar Sriganesh Kamath Priyadharshi Dixit Craniotomy in Klippel-Trenaunay syndrome: Concerns and challenges Indian Journal of Anaesthesia chiari malformation klippel-trenaunay syndrome neurosurgery |
author_facet |
R P Sangeetha Nisha Baskar Sriganesh Kamath Priyadharshi Dixit |
author_sort |
R P Sangeetha |
title |
Craniotomy in Klippel-Trenaunay syndrome: Concerns and challenges |
title_short |
Craniotomy in Klippel-Trenaunay syndrome: Concerns and challenges |
title_full |
Craniotomy in Klippel-Trenaunay syndrome: Concerns and challenges |
title_fullStr |
Craniotomy in Klippel-Trenaunay syndrome: Concerns and challenges |
title_full_unstemmed |
Craniotomy in Klippel-Trenaunay syndrome: Concerns and challenges |
title_sort |
craniotomy in klippel-trenaunay syndrome: concerns and challenges |
publisher |
Wolters Kluwer Medknow Publications |
series |
Indian Journal of Anaesthesia |
issn |
0019-5049 0976-2817 |
publishDate |
2019-01-01 |
description |
Klippel-Trenaunay syndrome (KTS) is a rare congenital disorder characterised by cutaneous capillary malformations, soft tissue and bone hypertrophy and venous varicosities. The coexistence of Chiari 1 malformation and an intracranial tumour has been rarely reported in the literature. Multisystem involvement of this syndrome mandates adequate preparation and planning, with meticulous conduct of anaesthesia to achieve favourable outcomes. We report a case of KTS syndrome with Chiari 1 malformation who had presented for craniotomy, and thereby discuss the challenges faced during anaesthetic management of these patients for major surgeries. |
topic |
chiari malformation klippel-trenaunay syndrome neurosurgery |
url |
http://www.ijaweb.org/article.asp?issn=0019-5049;year=2019;volume=63;issue=12;spage=1033;epage=1035;aulast=Sangeetha |
work_keys_str_mv |
AT rpsangeetha craniotomyinklippeltrenaunaysyndromeconcernsandchallenges AT nishabaskar craniotomyinklippeltrenaunaysyndromeconcernsandchallenges AT sriganeshkamath craniotomyinklippeltrenaunaysyndromeconcernsandchallenges AT priyadharshidixit craniotomyinklippeltrenaunaysyndromeconcernsandchallenges |
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