Cortical Frontoparietal Network Dysfunction in CHMP2B-Frontotemporal Dementia
A rare cause of inherited frontotemporal dementia (FTD) is a mutation in the CHMP2B gene on chromosome 3 leading to the autosomal dominantly inherited FTD (CHMP2B-FTD). Since CHMP2B-FTD is clinically well-characterized, and patients show a distinct pattern of executive dysfunction, the condition off...
Main Authors: | Christian Sandøe Musaeus, Jette Stokholm Pedersen, Troels Wesenberg Kjær, Peter Johannsen, Gunhild Waldemar, Maria Joy Normann Haverberg, Theis Bacher, Jørgen Erik Nielsen, Peter Roos, The FReJA Consortium, S Gydesen, J Brown, AM Isaacs, J Collinge, A Gade, E Englund, E Fisher, TT Nielsen, T Thusgaard, I Holm |
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Format: | Article |
Language: | English |
Published: |
Frontiers Media S.A.
2021-09-01
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Series: | Frontiers in Aging Neuroscience |
Subjects: | |
Online Access: | https://www.frontiersin.org/articles/10.3389/fnagi.2021.714220/full |
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