Isolated Hypoplasia of Left Pulmonary Artery with Agenesis of Left Lobe of Thyroid: A Case Report
Isolated Unilateral hypoplasia or agenesis of a branch of pulmonary artery is very rare. It is usually seen associated with congenital heart diseases such as tetralogy of Fallot, atrial septal defect, coarctation of the aorta, right aortic arch, truncus arteriosus, patent ductus arteriosus and pul...
| Main Authors: | , , , |
|---|---|
| Format: | Article |
| Language: | English |
| Published: |
JCDR Research and Publications Private Limited
2016-12-01
|
| Series: | Journal of Clinical and Diagnostic Research |
| Subjects: | |
| Online Access: | https://jcdr.net/articles/PDF/9093/23224_CE(Ra1)_F(Sh)_PF1(PGAK)_PFA(AK)_PF2(PAG).pdf |
| Summary: | Isolated Unilateral hypoplasia or agenesis of a branch of pulmonary artery is very rare. It is usually seen associated with congenital heart
diseases such as tetralogy of Fallot, atrial septal defect, coarctation of the aorta, right aortic arch, truncus arteriosus, patent ductus
arteriosus and pulmonary atresia. It occurs as a result of lack of embryological development of either the left or right sixth aortic arch
and has been found to present itself with various clinical manifestations as during childhood it presents as contralateral pulmonary
hypertension and in adults as haemoptysis. Early diagnosis and early surgical indication avoids the evolution of pulmonary hypertension
to unfavourble state of more severe and progressive degrees and also prevents the development of pulmonary systemic collateral
circulation, which is mainly responsible for subsequent haemoptysis in the adulthood. We hereby, report the case of an infant who
presented with features of lower respiratory tract infection and later diagnosed as isolated congenital hypoplasia of left pulmonary artery
and hence planned for proper follow-up for early surgery thereby preventing complications in the future. |
|---|---|
| ISSN: | 2249-782X 0973-709X |