Anesthesia management of pediatric dentistry patients with cardiofaciocutaneous syndrome: a case report

Anesthesia management of pediatric dentistry patients with cardiofaciocutaneous syndrome: a case report

Cardiofaciocutaneous syndrome is a rare syndrome characterized by particular craniofacial features, cardiac abnormalities, and multiple organ diseases. Patients present with pulmonary stenosis, hypertrophic cardiomyopathy, short neck, micrognathia, laryngomalacia, and tracheomalacia. These condition...

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Main Authors: Gian Luigi Gonnella, Pietro Paolo Giuri, Bruno Antonio Zanfini, Matteo Biancone, Luciano Frassanito, Cristina Olivieri, Gaetano Draisci
Format: Article
Language:English
Published: Elsevier 2021-03-01
Series:Brazilian Journal of Anesthesiology
Subjects:
Cardiofaciocutaneous syndrome
Airway management
Congenital heart defects
Online Access:http://www.sciencedirect.com/science/article/pii/S0104001421000270
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spelling doaj-db9861b711494988b6332aed45f4e5be2021-04-24T05:55:55ZengElsevierBrazilian Journal of Anesthesiology0104-00142021-03-01712178180Anesthesia management of pediatric dentistry patients with cardiofaciocutaneous syndrome: a case reportGian Luigi Gonnella0Pietro Paolo Giuri1Bruno Antonio Zanfini2Matteo Biancone3Luciano Frassanito4Cristina Olivieri5Gaetano Draisci6Corresponding author.; Policlinico Universitario Agostino Gemelli, “A. Gemelli” University Polyclinic Foundation, Catholic University of the Sacred Heart, Department of Anesthesiology and Intensive Care Medicine, Rome, ItalyPoliclinico Universitario Agostino Gemelli, “A. Gemelli” University Polyclinic Foundation, Catholic University of the Sacred Heart, Department of Anesthesiology and Intensive Care Medicine, Rome, ItalyPoliclinico Universitario Agostino Gemelli, “A. Gemelli” University Polyclinic Foundation, Catholic University of the Sacred Heart, Department of Anesthesiology and Intensive Care Medicine, Rome, ItalyPoliclinico Universitario Agostino Gemelli, “A. Gemelli” University Polyclinic Foundation, Catholic University of the Sacred Heart, Department of Anesthesiology and Intensive Care Medicine, Rome, ItalyPoliclinico Universitario Agostino Gemelli, “A. Gemelli” University Polyclinic Foundation, Catholic University of the Sacred Heart, Department of Anesthesiology and Intensive Care Medicine, Rome, ItalyPoliclinico Universitario Agostino Gemelli, “A. Gemelli” University Polyclinic Foundation, Catholic University of the Sacred Heart, Department of Anesthesiology and Intensive Care Medicine, Rome, ItalyPoliclinico Universitario Agostino Gemelli, “A. Gemelli” University Polyclinic Foundation, Catholic University of the Sacred Heart, Department of Anesthesiology and Intensive Care Medicine, Rome, ItalyCardiofaciocutaneous syndrome is a rare syndrome characterized by particular craniofacial features, cardiac abnormalities, and multiple organ diseases. Patients present with pulmonary stenosis, hypertrophic cardiomyopathy, short neck, micrognathia, laryngomalacia, and tracheomalacia. These conditions may strongly influence patient perioperative outcomes. We describe a 15-year-old child with cardiofaciocutaneous syndrome presenting for a dentistry procedure. She had an uneventful perioperative and postoperative course except for difficult airway management.http://www.sciencedirect.com/science/article/pii/S0104001421000270Cardiofaciocutaneous syndromeAirway managementCongenital heart defects
collection DOAJ
language English
format Article
sources DOAJ
author Gian Luigi Gonnella
Pietro Paolo Giuri
Bruno Antonio Zanfini
Matteo Biancone
Luciano Frassanito
Cristina Olivieri
Gaetano Draisci
spellingShingle Gian Luigi Gonnella
Pietro Paolo Giuri
Bruno Antonio Zanfini
Matteo Biancone
Luciano Frassanito
Cristina Olivieri
Gaetano Draisci
Anesthesia management of pediatric dentistry patients with cardiofaciocutaneous syndrome: a case report
Brazilian Journal of Anesthesiology
Cardiofaciocutaneous syndrome
Airway management
Congenital heart defects
author_facet Gian Luigi Gonnella
Pietro Paolo Giuri
Bruno Antonio Zanfini
Matteo Biancone
Luciano Frassanito
Cristina Olivieri
Gaetano Draisci
author_sort Gian Luigi Gonnella
title Anesthesia management of pediatric dentistry patients with cardiofaciocutaneous syndrome: a case report
title_short Anesthesia management of pediatric dentistry patients with cardiofaciocutaneous syndrome: a case report
title_full Anesthesia management of pediatric dentistry patients with cardiofaciocutaneous syndrome: a case report
title_fullStr Anesthesia management of pediatric dentistry patients with cardiofaciocutaneous syndrome: a case report
title_full_unstemmed Anesthesia management of pediatric dentistry patients with cardiofaciocutaneous syndrome: a case report
title_sort anesthesia management of pediatric dentistry patients with cardiofaciocutaneous syndrome: a case report
publisher Elsevier
series Brazilian Journal of Anesthesiology
issn 0104-0014
publishDate 2021-03-01
description Cardiofaciocutaneous syndrome is a rare syndrome characterized by particular craniofacial features, cardiac abnormalities, and multiple organ diseases. Patients present with pulmonary stenosis, hypertrophic cardiomyopathy, short neck, micrognathia, laryngomalacia, and tracheomalacia. These conditions may strongly influence patient perioperative outcomes. We describe a 15-year-old child with cardiofaciocutaneous syndrome presenting for a dentistry procedure. She had an uneventful perioperative and postoperative course except for difficult airway management.
topic Cardiofaciocutaneous syndrome
Airway management
Congenital heart defects
url http://www.sciencedirect.com/science/article/pii/S0104001421000270
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