Trabeculectomy with scleral patch graft for advanced glaucoma in ehler–danlos syndrome

• Main Authors: Dhanya Cheriyath, Shabana Bharathi, Ganesh V Raman
• Format: Article
• Language: English
• Published: Wolters Kluwer Medknow Publications 2016-01-01
• Series: Kerala Journal of Ophthalmology
• Subjects: Ehler–Danlos syndrome (EDS); intractable glaucoma; scleral patch graft; trabeculectomy
• Online Access: http://www.kjophthal.com/article.asp?issn=0976-6677;year=2016;volume=28;issue=2;spage=142;epage=144;aulast=Cheriyath

We report a case of secondary glaucoma in Ehler–Danlos syndrome (EDS) Type VI, which was uncontrolled with maximal medical therapy, and was subsequently managed surgically. EDS comprises a subgroup of heritable connective tissue disorders characterized by generalized joint hypermobility, skin hyperextensibility, and tissue fragility. The surgical challenges in these patients are presence of scleral thinning, vascular fragility, and poor wound healing. Surgical intervention such as trabeculectomy in EDS has not been reported in the literature. With this case report, we share our trials and tribulations in managing this patient with trabeculectomy without antimetabolites, with unexpected modification in the surgery and success.