Focal actinic porokeratosis: A new variant?

Porokeratosis is an autosomal dominantly transmitted disorder of keratinization predominantly affecting trunk and extremities. Many clinical variants have been described having a common histopathological feature of coronoid lamella-porokeratosis of Mibelli, superficial disseminate, disseminated supe...

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Main Authors: Pihu Sethi, Neeti Kumari, Bhuvan Adhlakha, Amrinder Jit Kanwar
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2018-01-01
Series:Indian Journal of Paediatric Dermatology
Subjects:
Online Access:http://www.ijpd.in/article.asp?issn=2319-7250;year=2018;volume=19;issue=3;spage=272;epage=273;aulast=Sethi
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spelling doaj-dfa784c6bca6477f8d9d1077778661772020-11-24T20:58:44ZengWolters Kluwer Medknow PublicationsIndian Journal of Paediatric Dermatology2319-72502018-01-0119327227310.4103/ijpd.IJPD_9_17Focal actinic porokeratosis: A new variant?Pihu SethiNeeti KumariBhuvan AdhlakhaAmrinder Jit KanwarPorokeratosis is an autosomal dominantly transmitted disorder of keratinization predominantly affecting trunk and extremities. Many clinical variants have been described having a common histopathological feature of coronoid lamella-porokeratosis of Mibelli, superficial disseminate, disseminated superficial actinic porokeratosis, linear porokeratosis and punctuate palmoplantar porokeratosis. We present a case of 16-year-old female who had focal lesions of porokeratosis aggravated by sun exposure, over alae of nose confirmed by histopathology. The previous reports show quite a number of cases of isolated lesions of the disease on nose and perinasal area. This article highlights the actinic nature of focal facial porokeratosis.http://www.ijpd.in/article.asp?issn=2319-7250;year=2018;volume=19;issue=3;spage=272;epage=273;aulast=SethiCoronoid lamellafocal actinicporokeratosis
collection DOAJ
language English
format Article
sources DOAJ
author Pihu Sethi
Neeti Kumari
Bhuvan Adhlakha
Amrinder Jit Kanwar
spellingShingle Pihu Sethi
Neeti Kumari
Bhuvan Adhlakha
Amrinder Jit Kanwar
Focal actinic porokeratosis: A new variant?
Indian Journal of Paediatric Dermatology
Coronoid lamella
focal actinic
porokeratosis
author_facet Pihu Sethi
Neeti Kumari
Bhuvan Adhlakha
Amrinder Jit Kanwar
author_sort Pihu Sethi
title Focal actinic porokeratosis: A new variant?
title_short Focal actinic porokeratosis: A new variant?
title_full Focal actinic porokeratosis: A new variant?
title_fullStr Focal actinic porokeratosis: A new variant?
title_full_unstemmed Focal actinic porokeratosis: A new variant?
title_sort focal actinic porokeratosis: a new variant?
publisher Wolters Kluwer Medknow Publications
series Indian Journal of Paediatric Dermatology
issn 2319-7250
publishDate 2018-01-01
description Porokeratosis is an autosomal dominantly transmitted disorder of keratinization predominantly affecting trunk and extremities. Many clinical variants have been described having a common histopathological feature of coronoid lamella-porokeratosis of Mibelli, superficial disseminate, disseminated superficial actinic porokeratosis, linear porokeratosis and punctuate palmoplantar porokeratosis. We present a case of 16-year-old female who had focal lesions of porokeratosis aggravated by sun exposure, over alae of nose confirmed by histopathology. The previous reports show quite a number of cases of isolated lesions of the disease on nose and perinasal area. This article highlights the actinic nature of focal facial porokeratosis.
topic Coronoid lamella
focal actinic
porokeratosis
url http://www.ijpd.in/article.asp?issn=2319-7250;year=2018;volume=19;issue=3;spage=272;epage=273;aulast=Sethi
work_keys_str_mv AT pihusethi focalactinicporokeratosisanewvariant
AT neetikumari focalactinicporokeratosisanewvariant
AT bhuvanadhlakha focalactinicporokeratosisanewvariant
AT amrinderjitkanwar focalactinicporokeratosisanewvariant
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