Birthmark: Journey from aesthetic to unalluring

Birthmark: Journey from aesthetic to unalluring

Encephalotrigeminal Angiomatosis, also known as Sturge Weber Syndrome (SWS), Dimitri disease, Sturge Kalischer Weber Syndrome is specifically non familial, congenital rare disorder consisting of hamartomatous malformations that may affect eye, skin, and CNS. Failure of proper vascular development is...

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Bibliographic Details
Main Authors: Sakshi Sharma, Pratiksha Hada, Vikram Singh, Mamta Singh
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2020-01-01
Series:Journal of Indian Academy of Oral Medicine and Radiology
Subjects:
angiofibromas
encephalotrigeminal angiomatosis
neurocutaneous
portwine stain
sws
tram- track calcifications
Online Access:http://www.jiaomr.in/article.asp?issn=0972-1363;year=2020;volume=32;issue=3;spage=303;epage=307;aulast=Sharma
Description
Summary:Encephalotrigeminal Angiomatosis, also known as Sturge Weber Syndrome (SWS), Dimitri disease, Sturge Kalischer Weber Syndrome is specifically non familial, congenital rare disorder consisting of hamartomatous malformations that may affect eye, skin, and CNS. Failure of proper vascular development is believed to be the most likely cause of the condition. The malformed blood vessels may lead to port wine stains, epilepsy, and glaucoma depending on its location. We are presenting here a triad of case reports on Sturge Weber Syndrome representing individuals belonging to varied age groups.
ISSN:0972-1363

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