Birthmark: Journey from aesthetic to unalluring

• Main Authors: Sakshi Sharma, Pratiksha Hada, Vikram Singh, Mamta Singh
• Format: Article
• Language: English
• Published: Wolters Kluwer Medknow Publications 2020-01-01
• Series: Journal of Indian Academy of Oral Medicine and Radiology
• Subjects: angiofibromas; encephalotrigeminal angiomatosis; neurocutaneous; portwine stain; sws; tram- track calcifications
• Online Access: http://www.jiaomr.in/article.asp?issn=0972-1363;year=2020;volume=32;issue=3;spage=303;epage=307;aulast=Sharma

Encephalotrigeminal Angiomatosis, also known as Sturge Weber Syndrome (SWS), Dimitri disease, Sturge Kalischer Weber Syndrome is specifically non familial, congenital rare disorder consisting of hamartomatous malformations that may affect eye, skin, and CNS. Failure of proper vascular development is believed to be the most likely cause of the condition. The malformed blood vessels may lead to port wine stains, epilepsy, and glaucoma depending on its location. We are presenting here a triad of case reports on Sturge Weber Syndrome representing individuals belonging to varied age groups.