CORRECTION OF SEVERE DYSTROPHIC SCOLIOSIS IN NEUROFIBROMATOSIS 1 WITH POSTERIOR VERTEBRAL COLUMN RESECTION IN MULTIPLE LEVELS
ABSTRACT Objective To evaluate the results after multiple posterior vertebral column resection (PVCR) in patients with severe kyphoscoliosis secondary to neurofibromatosis type 1 (NF-1). Methods Retrospective study of 4 adult male patients, mean age of 26.5 years, with severe rigid deformity, mean...
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doaj-e167c400606449cda4d6c80010488f2d2020-11-25T02:11:17ZengSociedade Brasileira de Coluna (SBC)Coluna/Columna 2177-014X18318719110.1590/s1808-185120191803195306S1808-18512019000300187CORRECTION OF SEVERE DYSTROPHIC SCOLIOSIS IN NEUROFIBROMATOSIS 1 WITH POSTERIOR VERTEBRAL COLUMN RESECTION IN MULTIPLE LEVELSALDERICO GIRÃO CAMPOS DE BARROSLUÍS EDUARDO CARELLI TEIXEIRA DA SILVAJÚLIO ALVES PONTEGUSTAVO BORGES LAURINDO AZEVEDORENATO JOÃO MUNIZ TEIXEIRAANDRE LUIZ LOYELO BARCELLOSABSTRACT Objective To evaluate the results after multiple posterior vertebral column resection (PVCR) in patients with severe kyphoscoliosis secondary to neurofibromatosis type 1 (NF-1). Methods Retrospective study of 4 adult male patients, mean age of 26.5 years, with severe rigid deformity, mean kyphosis of 122º and scoliosis of 88º, through clinical analysis and complementary exams. Results The mean postoperative follow-up was 27 months. Three vertebrae were resected on average. Interbody consolidation of arthrodesis was confirmed by CT in all cases. The correction rates of sagittal and coronal deformities were 54.09% and 70.45%, respectively. Prior to surgery, all patients were neurologically intact and as a post-surgical complication one patient had motor deficit (ASIA D) and pneumothorax also occurred in two patients. Conclusions The correction of severe kyphoscoliosis in adult patients with NF-1 is technically demanding and is not free of major complications. However, in view of the limited possibility of correction of these deformities, multiple-level PVCR has proved to be a safe and effective technique. Level of evidence IV; Case Series.http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1808-18512019000300187&lng=en&tlng=enNeurofibromatoseCifoseOsteotomia |
collection |
DOAJ |
language |
English |
format |
Article |
sources |
DOAJ |
author |
ALDERICO GIRÃO CAMPOS DE BARROS LUÍS EDUARDO CARELLI TEIXEIRA DA SILVA JÚLIO ALVES PONTE GUSTAVO BORGES LAURINDO AZEVEDO RENATO JOÃO MUNIZ TEIXEIRA ANDRE LUIZ LOYELO BARCELLOS |
spellingShingle |
ALDERICO GIRÃO CAMPOS DE BARROS LUÍS EDUARDO CARELLI TEIXEIRA DA SILVA JÚLIO ALVES PONTE GUSTAVO BORGES LAURINDO AZEVEDO RENATO JOÃO MUNIZ TEIXEIRA ANDRE LUIZ LOYELO BARCELLOS CORRECTION OF SEVERE DYSTROPHIC SCOLIOSIS IN NEUROFIBROMATOSIS 1 WITH POSTERIOR VERTEBRAL COLUMN RESECTION IN MULTIPLE LEVELS Coluna/Columna Neurofibromatose Cifose Osteotomia |
author_facet |
ALDERICO GIRÃO CAMPOS DE BARROS LUÍS EDUARDO CARELLI TEIXEIRA DA SILVA JÚLIO ALVES PONTE GUSTAVO BORGES LAURINDO AZEVEDO RENATO JOÃO MUNIZ TEIXEIRA ANDRE LUIZ LOYELO BARCELLOS |
author_sort |
ALDERICO GIRÃO CAMPOS DE BARROS |
title |
CORRECTION OF SEVERE DYSTROPHIC SCOLIOSIS IN NEUROFIBROMATOSIS 1 WITH POSTERIOR VERTEBRAL COLUMN RESECTION IN MULTIPLE LEVELS |
title_short |
CORRECTION OF SEVERE DYSTROPHIC SCOLIOSIS IN NEUROFIBROMATOSIS 1 WITH POSTERIOR VERTEBRAL COLUMN RESECTION IN MULTIPLE LEVELS |
title_full |
CORRECTION OF SEVERE DYSTROPHIC SCOLIOSIS IN NEUROFIBROMATOSIS 1 WITH POSTERIOR VERTEBRAL COLUMN RESECTION IN MULTIPLE LEVELS |
title_fullStr |
CORRECTION OF SEVERE DYSTROPHIC SCOLIOSIS IN NEUROFIBROMATOSIS 1 WITH POSTERIOR VERTEBRAL COLUMN RESECTION IN MULTIPLE LEVELS |
title_full_unstemmed |
CORRECTION OF SEVERE DYSTROPHIC SCOLIOSIS IN NEUROFIBROMATOSIS 1 WITH POSTERIOR VERTEBRAL COLUMN RESECTION IN MULTIPLE LEVELS |
title_sort |
correction of severe dystrophic scoliosis in neurofibromatosis 1 with posterior vertebral column resection in multiple levels |
publisher |
Sociedade Brasileira de Coluna (SBC) |
series |
Coluna/Columna |
issn |
2177-014X |
description |
ABSTRACT Objective To evaluate the results after multiple posterior vertebral column resection (PVCR) in patients with severe kyphoscoliosis secondary to neurofibromatosis type 1 (NF-1). Methods Retrospective study of 4 adult male patients, mean age of 26.5 years, with severe rigid deformity, mean kyphosis of 122º and scoliosis of 88º, through clinical analysis and complementary exams. Results The mean postoperative follow-up was 27 months. Three vertebrae were resected on average. Interbody consolidation of arthrodesis was confirmed by CT in all cases. The correction rates of sagittal and coronal deformities were 54.09% and 70.45%, respectively. Prior to surgery, all patients were neurologically intact and as a post-surgical complication one patient had motor deficit (ASIA D) and pneumothorax also occurred in two patients. Conclusions The correction of severe kyphoscoliosis in adult patients with NF-1 is technically demanding and is not free of major complications. However, in view of the limited possibility of correction of these deformities, multiple-level PVCR has proved to be a safe and effective technique. Level of evidence IV; Case Series. |
topic |
Neurofibromatose Cifose Osteotomia |
url |
http://www.scielo.br/scielo.php?script=sci_arttext&pid=S1808-18512019000300187&lng=en&tlng=en |
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