Extra-Abdominal Desmoid Tumors Associated with Familial Adenomatous Polyposis

Extra-abdominal desmoid tumors are a significant cause of morbidity in patients with familial adenomatous polyposis syndrome. Understanding of the basic biology and natural history of these tumors has increased substantially over the past decade. Accordingly, medical and surgical management of desmo...

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Main Authors: George T. Calvert, Michael J. Monument, Randall W. Burt, Kevin B. Jones, R. Lor Randall
Format: Article
Language:English
Published: Hindawi Limited 2012-01-01
Series:Sarcoma
Online Access:http://dx.doi.org/10.1155/2012/726537
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spelling doaj-e49bb2482ebd48648861a3f2d781701b2020-11-24T20:58:06ZengHindawi LimitedSarcoma1357-714X1369-16432012-01-01201210.1155/2012/726537726537Extra-Abdominal Desmoid Tumors Associated with Familial Adenomatous PolyposisGeorge T. Calvert0Michael J. Monument1Randall W. Burt2Kevin B. Jones3R. Lor Randall4Department of Orthopaedics and Huntsman Cancer Institute, The University of Utah, Salt Lake City, UT 84112, USADepartment of Orthopaedics and Huntsman Cancer Institute, The University of Utah, Salt Lake City, UT 84112, USADepartment of Medicine and Huntsman Cancer Institute, The University of Utah, Salt Lake City, UT 84112, USADepartment of Orthopaedics and Huntsman Cancer Institute, The University of Utah, Salt Lake City, UT 84112, USADepartment of Orthopaedics and Huntsman Cancer Institute, The University of Utah, Salt Lake City, UT 84112, USAExtra-abdominal desmoid tumors are a significant cause of morbidity in patients with familial adenomatous polyposis syndrome. Understanding of the basic biology and natural history of these tumors has increased substantially over the past decade. Accordingly, medical and surgical management of desmoid tumors has also evolved. This paper analyzes recent evidence pertaining to the epidemiology, molecular biology, histopathology, screening, and treatment of extra-abdominal desmoid tumors associated with familial adenomatous polyposis syndrome.http://dx.doi.org/10.1155/2012/726537
collection DOAJ
language English
format Article
sources DOAJ
author George T. Calvert
Michael J. Monument
Randall W. Burt
Kevin B. Jones
R. Lor Randall
spellingShingle George T. Calvert
Michael J. Monument
Randall W. Burt
Kevin B. Jones
R. Lor Randall
Extra-Abdominal Desmoid Tumors Associated with Familial Adenomatous Polyposis
Sarcoma
author_facet George T. Calvert
Michael J. Monument
Randall W. Burt
Kevin B. Jones
R. Lor Randall
author_sort George T. Calvert
title Extra-Abdominal Desmoid Tumors Associated with Familial Adenomatous Polyposis
title_short Extra-Abdominal Desmoid Tumors Associated with Familial Adenomatous Polyposis
title_full Extra-Abdominal Desmoid Tumors Associated with Familial Adenomatous Polyposis
title_fullStr Extra-Abdominal Desmoid Tumors Associated with Familial Adenomatous Polyposis
title_full_unstemmed Extra-Abdominal Desmoid Tumors Associated with Familial Adenomatous Polyposis
title_sort extra-abdominal desmoid tumors associated with familial adenomatous polyposis
publisher Hindawi Limited
series Sarcoma
issn 1357-714X
1369-1643
publishDate 2012-01-01
description Extra-abdominal desmoid tumors are a significant cause of morbidity in patients with familial adenomatous polyposis syndrome. Understanding of the basic biology and natural history of these tumors has increased substantially over the past decade. Accordingly, medical and surgical management of desmoid tumors has also evolved. This paper analyzes recent evidence pertaining to the epidemiology, molecular biology, histopathology, screening, and treatment of extra-abdominal desmoid tumors associated with familial adenomatous polyposis syndrome.
url http://dx.doi.org/10.1155/2012/726537
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AT randallwburt extraabdominaldesmoidtumorsassociatedwithfamilialadenomatouspolyposis
AT kevinbjones extraabdominaldesmoidtumorsassociatedwithfamilialadenomatouspolyposis
AT rlorrandall extraabdominaldesmoidtumorsassociatedwithfamilialadenomatouspolyposis
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