Uhl′s anomaly: Absence of the right ventricular myocardium

Uhl′s anomaly: Absence of the right ventricular myocardium

We report a case of Uhl′s anomaly in a 3-week-old infant that underwent central shunt placement, patent duct us arteriosus and main pulmonary artery ligation. The infant presented with room air saturation of 43%, dilated right ventricle with decreased function and dilated right atrium. Diagnosis was...

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Bibliographic Details
Main Authors: Joanna Ganczar, Robert English
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2015-01-01
Series:Annals of Pediatric Cardiology
Subjects:
Cyanosis in an infant
right-sided heart failure
right ventricular dysfunction
Uhl′sanomaly
Online Access:http://www.annalspc.com/article.asp?issn=0974-2069;year=2015;volume=8;issue=1;spage=71;epage=73;aulast=Ganczar
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spelling doaj-e6d671fe26ed4d83896753da981213c72020-11-24T21:15:38ZengWolters Kluwer Medknow PublicationsAnnals of Pediatric Cardiology0974-20692015-01-0181717310.4103/0974-2069.149529Uhl′s anomaly: Absence of the right ventricular myocardiumJoanna GanczarRobert EnglishWe report a case of Uhl′s anomaly in a 3-week-old infant that underwent central shunt placement, patent duct us arteriosus and main pulmonary artery ligation. The infant presented with room air saturation of 43%, dilated right ventricle with decreased function and dilated right atrium. Diagnosis was established with a myocardial biopsy.http://www.annalspc.com/article.asp?issn=0974-2069;year=2015;volume=8;issue=1;spage=71;epage=73;aulast=GanczarCyanosis in an infantright-sided heart failureright ventricular dysfunctionUhl′sanomaly
collection DOAJ
language English
format Article
sources DOAJ
author Joanna Ganczar
Robert English
spellingShingle Joanna Ganczar
Robert English
Uhl′s anomaly: Absence of the right ventricular myocardium
Annals of Pediatric Cardiology
Cyanosis in an infant
right-sided heart failure
right ventricular dysfunction
Uhl′sanomaly
author_facet Joanna Ganczar
Robert English
author_sort Joanna Ganczar
title Uhl′s anomaly: Absence of the right ventricular myocardium
title_short Uhl′s anomaly: Absence of the right ventricular myocardium
title_full Uhl′s anomaly: Absence of the right ventricular myocardium
title_fullStr Uhl′s anomaly: Absence of the right ventricular myocardium
title_full_unstemmed Uhl′s anomaly: Absence of the right ventricular myocardium
title_sort uhl′s anomaly: absence of the right ventricular myocardium
publisher Wolters Kluwer Medknow Publications
series Annals of Pediatric Cardiology
issn 0974-2069
publishDate 2015-01-01
description We report a case of Uhl′s anomaly in a 3-week-old infant that underwent central shunt placement, patent duct us arteriosus and main pulmonary artery ligation. The infant presented with room air saturation of 43%, dilated right ventricle with decreased function and dilated right atrium. Diagnosis was established with a myocardial biopsy.
topic Cyanosis in an infant
right-sided heart failure
right ventricular dysfunction
Uhl′sanomaly
url http://www.annalspc.com/article.asp?issn=0974-2069;year=2015;volume=8;issue=1;spage=71;epage=73;aulast=Ganczar
work_keys_str_mv AT joannaganczar uhlsanomalyabsenceoftherightventricularmyocardium
AT robertenglish uhlsanomalyabsenceoftherightventricularmyocardium
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