Lipofuscinose ceróide neuronal: achados clínicos e neurorradiológicos Neuronal ceroid lipofuscinosis: clinical and neuroradiological findings

Lipofuscinose ceróide neuronal: achados clínicos e neurorradiológicos Neuronal ceroid lipofuscinosis: clinical and neuroradiological findings

Lipofuscinose ceróide neuronal (LCN) constitui um grupo de doenças neurodegenerativas caracterizadas pelo depósito anormal de uma substância autofluorescente de lipopigmentos, que lembra ceróide e lipofuscina, dentro dos lisossomos dos neurônios e outros tipos de células. Os principais subtipos feno...

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Bibliographic Details
Main Authors:	Rômulo Lopes Gama, Mauro Nakayama, Daniel Gurgel Fernandes Távora, Thereza Christina de Lara Alvim, Cleto Dantas Nogueira, Dalton Portugal
Format:	Article
Language:	English
Published:	Academia Brasileira de Neurologia (ABNEURO) 2007-06-01
Series:	Arquivos de Neuro-Psiquiatria
Subjects:	lipofuscinose ceróide neuronal doença lisossômica de depósito achados neurorradiológicos neuronal ceroid lipofuscinosis lysosomal storage disease neuroradiological findings
Online Access:	http://www.scielo.br/scielo.php?script=sci_arttext&pid=S0004-282X2007000200025

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