The portopulmonary hypertension: an overview from diagnosis to treatment

Portopulmonary hypertension (POPH) refers to the condition of pulmonary arterial hypertension (PAH) in association with portal hypertension. Among patients with portal hypertension, reported incidence rates of POPH range from 2 to 10% and long-term prognosis in cases of- POPH is poor. Fundamental is...

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Bibliographic Details
Main Authors: Andrea Salzano, Domenico Sirico, Luisa Golia, Valentina Faga, Martina Flora, Eduardo Bossone, Antonio Cittadini
Format: Article
Language:English
Published: PAGEPress Publications 2015-11-01
Series:Monaldi Archives for Chest Disease
Subjects:
Online Access:https://www.monaldi-archives.org/index.php/macd/article/view/81
Description
Summary:Portopulmonary hypertension (POPH) refers to the condition of pulmonary arterial hypertension (PAH) in association with portal hypertension. Among patients with portal hypertension, reported incidence rates of POPH range from 2 to 10% and long-term prognosis in cases of- POPH is poor. Fundamental issues of management of POPH include identification of patients likely to benefit from liver transplantation (LTx) and treatment with specific pulmonary vasodilators before and after LTx. This review presents as an overview of the current knowledge on the epidemiology, diagnosis, treatment and prognosis of patients with portopulmonary hypertension.
ISSN:1122-0643
2532-5264