Caractérisation de modèles pouvant modifier le métabolisme énergétique mitochondrial : syndrome de Leigh et haplogroupes mitochondriaux
Un des rôles de la mitochondrie, qui possède son propre ADN (ADNmt), est la production de l'énergie nécessaire à la cellule, qu'elle synthétise sous forme d'ATP grâce aux oxydations phosphorylantes (OXPHOS). Ainsi, une altération du métabolisme énergétique mitochondrial peut provoquer...
Main Author: | Da Costa, Barbara |
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Other Authors: | Toulouse 3 |
Language: | fr |
Published: |
2017
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Subjects: | |
Online Access: | http://www.theses.fr/2017TOU30325/document |
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