Distinct expression of functionally glycosylated alpha-dystroglycan in muscle and non-muscle tissues of FKRP mutant mice.

by Anthony Blaeser, Hiroyuki Awano, Pei Lu, Qi-Long Lu
Published 2018-01-01

Progressive Dystrophic Pathology in Diaphragm and Impairment of Cardiac Function in FKRP P448L Mutant Mice.

by Anthony Blaeser, Hiroyuki Awano, Bo Wu, Qi-Long Lu
Published 2016-01-01

Ribitol restores functionally glycosylated α-dystroglycan and improves muscle function in dystrophic FKRP-mutant mice

by Marcela P. Cataldi, Peijuan Lu, Anthony Blaeser, Qi Long Lu
Published 2018-08-01

ISPD Overexpression Enhances Ribitol-Induced Glycosylation of α-Dystroglycan in Dystrophic FKRP Mutant Mice

by Marcela P. Cataldi, Anthony Blaeser, Peijuan Lu, Victoria Leroy, Qi Long Lu
Published 2020-06-01

Skeletal, cardiac, and respiratory muscle function and histopathology in the P448Lneo− mouse model of FKRP-deficient muscular dystrophy

by Qing Yu, Melissa Morales, Ning Li, Alexander G. Fritz, Ren Ruobing, Anthony Blaeser, Ershia Francois, Qi-Long Lu, Kanneboyina Nagaraju, Christopher F. Spurney
Published 2018-04-01