Emerging Concepts in Vector Development for Glial Gene Therapy: Implications for Leukodystrophies

by Georg von Jonquieres, Caroline D. Rae, Gary D. Housley
Published 2021-06-01

Loss of central auditory processing in a mouse model of Canavan disease.

by Georg von Jonquieres, Kristina E Froud, Claudia B Klugmann, Ann C Y Wong, Gary D Housley, Matthias Klugmann
Published 2014-01-01

Gene therapy mediated seizure suppression in Genetic Generalised Epilepsy: Neuropeptide Y overexpression in a rat model

by Kim L. Powell, Xavier Fitzgerald, Claire Shallue, Valentina Jovanovska, Matthias Klugmann, Georg Von Jonquieres, Terence J. O'Brien, Margaret J. Morris
Published 2018-05-01

Australian Scorpion <i>Hormurus waigiensis</i> Venom Fractions Show Broad Bioactivity Through Modulation of Bio-Impedance and Cytosolic Calcium

by David M. Housley, Jeremy L. Pinyon, Georg von Jonquieres, Chamini J. Perera, Michael Smout, Michael J. Liddell, Ernest A. Jennings, David Wilson, Gary D. Housley
Published 2020-04-01

Expression Pattern of the Aspartyl-tRNA Synthetase DARS in the Human Brain

by Dominik Fröhlich, Alexandra K. Suchowerska, Carola Voss, Ruojie He, Ruojie He, Ernst Wolvetang, Georg von Jonquieres, Cas Simons, Thomas Fath, Gary D. Housley, Matthias Klugmann
Published 2018-03-01

Glial promoter selectivity following AAV-delivery to the immature brain.

by Georg von Jonquieres, Nadine Mersmann, Claudia Bettina Klugmann, Anne Editha Harasta, Beat Lutz, Orla Teahan, Gary David Housley, Dominik Fröhlich, Eva-Maria Krämer-Albers, Matthias Klugmann
Published 2013-01-01

In vivo characterization of the aspartyl-tRNA synthetase DARS: Homing in on the leukodystrophy HBSL

by Dominik Fröhlich, Alexandra K. Suchowerska, Ziggy H.T. Spencer, Georg von Jonquieres, Claudia B. Klugmann, Andre Bongers, Fabien Delerue, Holly Stefen, Lars M. Ittner, Thomas Fath, Gary D. Housley, Matthias Klugmann
Published 2017-01-01

Behavioral and Neurochemical Phenotyping of Mice Incapable of Homer1a Induction

by Michael C. Datko, Jia-Hua Hu, Melanie Williams, Cindy M. Reyes, Kevin D. Lominac, Georg von Jonquieres, Matthias Klugmann, Paul F. Worley, Karen K. Szumlinski, Karen K. Szumlinski, Karen K. Szumlinski
Published 2017-11-01

Transgenic Analyses of Homer2 Function Within Nucleus Accumbens Subregions in the Regulation of Methamphetamine Reward and Reinforcement in Mice

by Chelsea N. Brown, Elissa K. Fultz, Sami Ferdousian, Sarina Rogers, Elijah Lustig, Ariana Page, John R. Shahin, Daniel M. Flaherty, Georg Von Jonquieres, Camron D. Bryant, Tod E. Kippin, Tod E. Kippin, Tod E. Kippin, Karen K. Szumlinski, Karen K. Szumlinski
Published 2020-02-01

Tau exacerbates excitotoxic brain damage in an animal model of stroke

by Mian Bi, Amadeus Gladbach, Janet van Eersel, Arne Ittner, Magdalena Przybyla, Annika van Hummel, Sook Wern Chua, Julia van der Hoven, Wei S. Lee, Julius Müller, Jasneet Parmar, Georg von Jonquieres, Holly Stefen, Ernesto Guccione, Thomas Fath, Gary D. Housley, Matthias Klugmann, Yazi D. Ke, Lars M. Ittner
Published 2017-09-01