Recent Advances in the Pathophysiology of Fatty Acid Oxidation Defects: Secondary Alterations of Bioenergetics and Mitochondrial Calcium Homeostasis Caused by the Accumulating Fatt...

by Alexandre Umpierrez Amaral, Alexandre Umpierrez Amaral, Moacir Wajner, Moacir Wajner, Moacir Wajner
Published 2020-11-01

The Role of Hyperhomocysteinemia in Disease

by Carmen R. Vargas PhD, Angela Sitta, Moacir Wajner MD, PhD
Published 2018-08-01

Detection of metabolic disorders in high-risk patients: a pilot study in Salvador, Bahia Detecção de doenças metabólicas em pacientes de alto-risco: estudo piloto em Salvador, Bahi...

by Maria Betânia Pereira, Gildásio Carvalho da Conceição, Janice C. Coelho, Moacir Wajner, Roberto Giugliani
Published 1997-06-01

Screening for organic acidurias and aminoacidopathies in high-risk Brazilian patients: Eleven-year experience of a reference center

by Moacir Wajner, Angela Sitta, Aline Kayser, Marion Deon, Ana C. Groehs, Daniella M. Coelho, Carmen R. Vargas
Published 2019-04-01

Astrocytic proliferation and mitochondrial dysfunction induced by accumulated glutaric acidemia I (GAI) metabolites: Possible implications for GAI pathogenesis

by Silvia Olivera, Anabel Fernandez, Alexandra Latini, Juan Carlos Rosillo, Gabriela Casanova, Moacir Wajner, Patricia Cassina, Luis Barbeito
Published 2008-12-01

Resveratrol protects C6 astrocyte cell line against hydrogen peroxide-induced oxidative stress through heme oxygenase 1.

by André Quincozes-Santos, Larissa Daniele Bobermin, Alexandra Latini, Moacir Wajner, Diogo Onofre Souza, Carlos-Alberto Gonçalves, Carmem Gottfried
Published 2013-01-01

Mechanistic Bases of Neurotoxicity Provoked by Fatty Acids Accumulating in MCAD and LCHAD Deficiencies

by Alexandre U. Amaral PhD, Cristiane Cecatto MSc, Janaína C. da Silva PhD, Alessandro Wajner PhD, Moacir Wajner MD, PhD
Published 2017-03-01

Acidúrias orgânicas: diagnóstico em pacientes de alto risco no Brasil Organic aciduria: diagnosis in high-risk Brazilian patients

by Moacir Wajner, Alethéa G. Barschak, Ana Paula Luft, Ricardo Pires, Eugênio Grillo, Alfredo Lohr, Carolina Funayama, Maria Teresa Sanseverino, Roberto Giugliani, Carmen R. Vargas
Published 2001-10-01

Acute Liver Failure Induces Glial Reactivity, Oxidative Stress and Impairs Brain Energy Metabolism in Rats

by Pedro Arend Guazzelli, Pedro Arend Guazzelli, Giordano Fabricio Cittolin-Santos, Giordano Fabricio Cittolin-Santos, Leo Anderson Meira-Martins, Mateus Grings, Yasmine Nonose, Gabriel S. Lazzarotto, Daniela Nogara, Jussemara S. da Silva, Fernanda U. Fontella, Moacir Wajner, Moacir Wajner, Guilhian Leipnitz, Diogo O. Souza, Diogo O. Souza, Adriano Martimbianco de Assis, Adriano Martimbianco de Assis
Published 2020-01-01

Increased glutamate receptor and transporter expression in the cerebral cortex and striatum of gcdh-/- mice: possible implications for the neuropathology of glutaric acidemia type...

by Valeska Lizzi Lagranha, Ursula Matte, Talita Giacomet de Carvalho, Bianca Seminotti, Carolina Coffi Pereira, David M Koeller, Michael Woontner, Stephen I Goodman, Diogo Onofre Gomes de Souza, Moacir Wajner
Published 2014-01-01

DNA damage in homocystinuria: 8-oxo‑,8‑dihydro‑2’-deoxyguanosine levels in cystathionine-β-synthase deficient patients and the in vitro protective effect of N-acetyl‑L‑cysteine...

by Camila Simioni Vanzin, Caroline Paula Mescka, Bruna Donida, Desirèe Padilha Marchetti, Carlos Eduardo Jacques, Tatiane Hauschild, Jéssica Lamberty Faverzani, Marion Deon, Dinara Moura, Jenifer Saffi, Daniella de Moura Coelho, Moacir Wajner, Angela T.S. Wyse, Carmen Regla Vargas
Published 2018-04-01

DNA damage in homocystinuria: 8-oxo‑,8‑dihydro‑2’-deoxyguanosine levels in cystathionine-β-synthase deficient patients and the in vitro protective effect of N-acetyl‑L‑cysteine...

by Camila Simioni Vanzin, Caroline Paula Mescka, Bruna Donida, Desirèe Padilha Marchetti, Carlos Eduardo Jacques, Tatiane Hauschild, Jéssica Lamberty Faverzani, Marion Deon, Dinara Moura, Jenifer Saffi, Daniella de Moura Coelho, Moacir Wajner, Angela T.S. Wyse, Carmen Regla Vargas
Published 2018-04-01