Hemophagocytic lymphohistiocytosis: a rare diagnosis, an even rarer opportunity to appraise our understanding of the immune system
The syndrome identified as hemophagocytic lymphohistiocytosis (HLH) poses a rather difficult challenge to the physician. HLH was initially described as a familial disorder,1 which was later associated with various genetic defects that affect the cytotoxic machinery of CD8+ T and NK cells,2 but it a...
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| Format: | Article |
| Language: | English |
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University of São Paulo
2015-03-01
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| Series: | Autopsy and Case Reports |
| Online Access: | http://www.revistas.usp.br/autopsy/article/view/98449 |