Ciliated conical epithelial cell protrusions point towards a diagnosis of primary ciliary dyskinesia

Abstract Background Primary ciliary dyskinesia can result from a number of different ciliary defects that adversely affect ciliary function resulting markedly reduced or absent mucociliary clearance. Improvement in diagnostic testing is an area of current research. During diagnostic evaluation of PC...

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Bibliographic Details
Main Authors: Chris O’Callaghan, Andrew Rutman, Gwyneth Williams, Neeta Kulkarni, Joseph Hayes, Robert A. Hirst
Format: Article
Language:English
Published: BMC 2018-06-01
Series:Respiratory Research
Subjects:
PCD
Online Access:http://link.springer.com/article/10.1186/s12931-018-0782-3