ANESTHETIC MANAGEMENT FOR A PATIENT WITH ACUTE INTERMITTENT PORPHYRIA

Acute intermittent porphyria is a rare metabolic disorder resulting from a partial deficiency of porphobilinogen deaminase, enzyme in the heme biosynthetic pathway. Its inheritance is autosomal dominant. A deficiency of porphobilinogen deaminase is not sufficient by its self to produce acute intermi...

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Bibliographic Details
Main Authors: Nenad Savić, Dragana Đorđević, Biljana Stošić, Lidija Đorđević, Angelina Bogićević, Anica Pavlović
Format: Article
Language:English
Published: University in Nis, Faculty of Medicine 2010-09-01
Series:Acta Medica Medianae
Subjects:
Online Access:http://publisher.medfak.ni.ac.rs/2010-html/3-broj/Angelina%20Bogicevic%20-%20Anestetic%20Management%2055-57.pdf