Functional and histopathological identification of the respiratory failure in a DMSXL transgenic mouse model of myotonic dystrophy
SUMMARY Acute and chronic respiratory failure is one of the major and potentially life-threatening features in individuals with myotonic dystrophy type 1 (DM1). Despite several clinical demonstrations showing respiratory problems in DM1 patients, the mechanisms are still not completely understood. T...
Main Authors: | , , , , |
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Format: | Article |
Language: | English |
Published: |
The Company of Biologists
2013-05-01
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Series: | Disease Models & Mechanisms |
Online Access: | http://dmm.biologists.org/content/6/3/622 |