Cyclosporine A in Ullrich Congenital Muscular Dystrophy: Long-Term Results

Six individuals with Ullrich congenital muscular dystrophy (UCMD) and mutations in the genes-encoding collagen VI, aging 5–9, received 3–5 mg/kg of cyclosporine A (CsA) daily for 1 to 3.2 years. The primary outcome measure was the muscle strength evaluated with a myometer and expressed as megalimbs....

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Main Authors: Luciano Merlini, Patrizia Sabatelli, Annarita Armaroli, Saverio Gnudi, Alessia Angelin, Paolo Grumati, Maria Elena Michelini, Andrea Franchella, Francesca Gualandi, Enrico Bertini, Nadir Mario Maraldi, Alessandra Ferlini, Paolo Bonaldo, Paolo Bernardi
Format: Article
Language:English
Published: Hindawi Limited 2011-01-01
Series:Oxidative Medicine and Cellular Longevity
Online Access:http://dx.doi.org/10.1155/2011/139194