Case Report: Dental Findings Can Aid in Early Diagnosis of APECED Syndrome

Autoimmune polyendocrinopathy-candidiasis-ectodermal dystrophy (APECED), also known as autoimmune polyglandular syndrome type 1 (APS-1), is a rare genetic disorder caused most often by biallelic mutations in the AIRE gene. Classic clinical findings of the disease are chronic mucocutaneous candidiasi...

Full description

Bibliographic Details
Main Authors: Laurie Brenchley, Elise M. N. Ferré, Monica M. Schmitt, Pamela J. Gardner, Michail S. Lionakis, Niki M. Moutsopoulos
Format: Article
Language:English
Published: Frontiers Media S.A. 2021-05-01
Series:Frontiers in Dental Medicine
Subjects:
Online Access:https://www.frontiersin.org/articles/10.3389/fdmed.2021.670624/full