Systematic review of drug effects in humans and models with surfactant-processing disease
Fibrotic interstitial pneumonias are a group of rare diseases characterised by distortion of lung interstitium. Patients with mutations in surfactant-processing genes, such as surfactant protein C (SFTPC), surfactant protein A1 and A2 (SFTPA1 and A2), ATP binding cassette A3 (ABCA3) and Hermansky–Pu...
| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
European Respiratory Society
2018-07-01
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| Series: | European Respiratory Review |
| Online Access: | http://err.ersjournals.com/content/27/149/170135.full |