Paroxysmal nocturnal hemoglobinuria: Diagnosis and management protocol

Paroxysmal nocturnal hemoglobinuria (PNH) is an acquired, rare clonal blood disorder, characterized by chronic intravascular hemolysis, bone marrow failure, renal failure and pulmonary hypertension, and a heightened risk of thrombotic complications. PNH etiology is an Υ-linked gene somatic mutation...

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Bibliographic Details
Main Authors: Abdul Kareem Almomen, Abdul Ghani Al Bakistani, Ahmad Alsaeed, Asma Al Olama, Ayman Hejazi, Christian Awarji, Fahed Almhareb, Faisal Alsayegh, Hazzaa Alzahrani, Mahmoud Almarashly, Mohammad Qari, Mohammad Aslam, Rania Seliem, Salam Al Kindi, Saud Abuharbesh, TareK Owaidah, Wafaa Bassuni
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2014-01-01
Series:Journal of Applied Hematology
Subjects:
Online Access:http://www.jahjournal.org/article.asp?issn=1658-5127;year=2014;volume=5;issue=2;spage=37;epage=44;aulast=Almomen