Hypertonic saline in people with cystic fibrosis: review of comparative studies and clinical practice
Abstract Cystic fibrosis (CF) is a multisystem disorder, caused by mutations in the CF transmembrane conductance regulator (CFTR) gene. These cause a reduced secretion of chloride, a marked absorption of sodium and, therefore, of water, through the epithelium, resulting in the formation of thickened...
Main Authors: | , , , , |
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Format: | Article |
Language: | English |
Published: |
BMC
2021-08-01
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Series: | Italian Journal of Pediatrics |
Subjects: | |
Online Access: | https://doi.org/10.1186/s13052-021-01117-1 |