Hypertonic saline in people with cystic fibrosis: review of comparative studies and clinical practice

Abstract Cystic fibrosis (CF) is a multisystem disorder, caused by mutations in the CF transmembrane conductance regulator (CFTR) gene. These cause a reduced secretion of chloride, a marked absorption of sodium and, therefore, of water, through the epithelium, resulting in the formation of thickened...

Full description

Bibliographic Details
Main Authors: Vito Terlizzi, Eleonora Masi, Michela Francalanci, Giovanni Taccetti, Diletta Innocenti
Format: Article
Language:English
Published: BMC 2021-08-01
Series:Italian Journal of Pediatrics
Subjects:
Online Access:https://doi.org/10.1186/s13052-021-01117-1