Hereditary Angioedema: a Challenging Diagnosis for the Gastroenterologist

Hereditary angioedema (HAE) caused by a deficiency of C1 esterase inhibitor enzyme (C1-INH) is a very rare, autosomal dominantly inherited genetic disorder, characterized by recurrent peripheral angioedema, painful abdominal attacks and episodes of laryngeal edema. Abdominal attacks are frequent sym...

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Bibliographic Details
Main Authors: Gábos Gabriella, Moldovan Dumitru, Dobru Daniela
Format: Article
Language:English
Published: Sciendo 2016-12-01
Series:Journal of Interdisciplinary Medicine
Subjects:
Online Access:https://doi.org/10.1515/jim-2016-0072