Wilms tumor, pleuropulmonary blastoma, and DICER1: case report and literature review

Abstract Background Pleuroblastoma (PPB) is a rare pediatric tumor which, in 30% of cases, is associated with cystic nephroma. It has been recently linked to the DICER1 mutation as part of a predisposition syndrome for various tumors. However, if DICER 1 anomalies have been reported in patients with...

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Bibliographic Details
Main Authors: Olivier Abbo, Kalitha Pinnagoda, Laurent Brouchet, Bertrand Leobon, Frédérique Savagner, Isabelle Oliver, Philippe Galinier, Marie-Pierre Castex, Marlène Pasquet
Format: Article
Language:English
Published: BMC 2018-08-01
Series:World Journal of Surgical Oncology
Subjects:
Online Access:http://link.springer.com/article/10.1186/s12957-018-1469-4