Cystic Fibrosis Liver Disease: Know More

Cystic fibrosis (CF) is a multisystem disease caused by mutations in the CF transmembrane conductance regulator (CFTR) gene. CFTR is expressed in the apical surface of cholangiocytes. Homozygous CFTR gene mutation results in viscous and acidic bile secretions secondary to deficient surface fluid and...

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Bibliographic Details
Main Authors: Siham Al Sinani, Sharef Al-Mulaabed, Khalid Al Naamani, Rabab Sultan
Format: Article
Language:English
Published: Oman Medical Specialty Board 2019-11-01
Series:Oman Medical Journal
Subjects:
Online Access:http://omjournal.org/articleDetails.aspx?coType=1&aId=2508