Treatment Strategies for GLILD in Common Variable Immunodeficiency: A Systematic Review

IntroductionBesides recurrent infections, a proportion of patients with Common Variable Immunodeficiency Disorders (CVID) may suffer from immune dysregulation such as granulomatous-lymphocytic interstitial lung disease (GLILD). The optimal treatment of this complication is currently unknown. Experie...

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Main Authors: Olivia A. C. Lamers, Bas M. Smits, Helen Louisa Leavis, Godelieve J. de Bree, Charlotte Cunningham-Rundles, Virgil A. S. H. Dalm, Hsi-en Ho, John R. Hurst, Hanna IJspeert, Sabine M. P. J. Prevaes, Alex Robinson, Astrid C. van Stigt, Suzanne Terheggen-Lagro, Annick A. J. M. van de Ven, Klaus Warnatz, Janneke H. H. M. van de Wijgert, Joris van Montfrans
Format: Article
Language:English
Published: Frontiers Media S.A. 2021-04-01
Series:Frontiers in Immunology
Subjects:
Online Access:https://www.frontiersin.org/articles/10.3389/fimmu.2021.606099/full