Lipidomic analysis of fibroblasts from Zellweger spectrum disorder patients identifies disease-specific phospholipid ratios[S]

Lipidomic analysis of fibroblasts from Zellweger spectrum disorder patients identifies disease-specific phospholipid ratios[S]

Peroxisomes are subcellular organelles involved in various metabolic processes, including fatty acid and phospholipid homeostasis. The Zellweger spectrum disorders (ZSDs) represent a group of diseases caused by a defect in the biogenesis of peroxisomes. Accordingly, cells from ZSD patients are expec...

Full description

Bibliographic Details
Main Authors: Katharina Herzog, Mia L. Pras-Raves, Martin A.T. Vervaart, Angela C.M. Luyf, Antoine H.C. van Kampen, Ronald J.A. Wanders, Hans R. Waterham, Frédéric M. Vaz
Format: Article
Language:English
Published: Elsevier 2016-08-01
Series:Journal of Lipid Research
Subjects:
peroxisomes
peroxisome biogenesis disorders
lipidomics
diagnosis
Online Access:http://www.sciencedirect.com/science/article/pii/S0022227520352160

Internet

http://www.sciencedirect.com/science/article/pii/S0022227520352160

Similar Items