Familial Hemophagocytic Lymphohistiocytosis Presenting as Hydrops Fetalis

Familial Hemophagocytic Lymphohistiocytosis Presenting as Hydrops Fetalis

Abstract Background Familial hemophagocytic lymphohistiocytosis (FLH) is an autosomal recessive disorder of immune regulation that leads to a hyperinflammatory syndrome. Fetal onset FHL is extremely rare and is considered to be the most severe form of FHL. Case We report a...

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Bibliographic Details
Main Authors: Sota Iwatani, Kazuya Uemura, Masami Mizobuchi, Seiji Yoshimoto, Keiichiro Kawasaki, Yoshiyuki Kosaka, Masayuki Hori, Takahiro Yasumi, Hideto Nakao
Format: Article
Language:English
Published: Thieme Medical Publishers, Inc. 2015-03-01
Series:American Journal of Perinatology Reports
Subjects:
familial hemophagocytic lymphohistiocytosis
hydrops fetalis
hepatosplenomegaly
cytopenia
immunosuppressive chemotherapy
Online Access:http://www.thieme-connect.de/DOI/DOI?10.1055/s-0034-1544110

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http://www.thieme-connect.de/DOI/DOI?10.1055/s-0034-1544110

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