Multiphoton Imaging of Ca<sup>2+</sup> Instability in Acute Myocardial Slices from a <i>RyR2</i><sup>R2474S</sup> Murine Model of Catecholaminergic Polymorphic Ventricular Tachycardia

Catecholaminergic Polymorphic Ventricular Tachycardia (CPVT) is a familial stress-induced arrhythmia syndrome, mostly caused by mutations in Ryanodine receptor 2 (<i>RyR</i>2), the sarcoplasmic reticulum (SR) Ca<sup>2+</sup> release channel in cardiomyocytes. Pathogenetic mut...

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Bibliographic Details
Main Authors: Giulia Borile, Tania Zaglia, Stephan E. Lehnart, Marco Mongillo
Format: Article
Language:English
Published: MDPI AG 2021-06-01
Series:Journal of Clinical Medicine
Subjects:
Online Access:https://www.mdpi.com/2077-0383/10/13/2821